EPA/630/Z-96/001
 Wednesday
 October 4, 1995
Part II

Environmental
Protection Agency
Proposed Guidelines for Neurotoxteity
Risk Assessment; Notice

-------
  52032
Federal Register
                                                                      October 4.  1995  -' Notices
  ENVIRONMENTAL PROTECTION
  AGENCY
  [FRL-&306-2]

  Proposed Guidelines for Neurotoxicity
  Risk Assessment
 AGENCY: Environmental Protection
 Agency (EPA).
 ACTION: Proposed guidelines for
 Neurotoxicity Risk Assessment and
 request for comments.

 SUMMARY: The U.S. Environmental
 Protection Agency (EPA; Agency) is
 today issuing proposed guidelines for
 assessing the risks for neurotoxicity
 from exposure to environmental agents.
 As background information for this
 guidance, this notice describes the
 scientific basis for concern about
 exposure to agents that causa
 nourotoxicity and outlines the general
 process for assessing potential risk to
 humans because of environmental
 contaminants.
  These proposed Guidelines for
 Neurotoxicity Risk Assessment
 (hereafter "Guidelines") are intended to
 guide Agency evaluation of agents that
 are suspected to causa neurotoxicity in
 line with the policies and procedures
 established in the statutes administered
 by the EPA. The Guidelines were
 developed as part of an interoffice
 guidelines development program under
 the auspices of the Risk Assessment
 Forum,  within EPA's Office of Research
 and Development Draft Guidelines
 wore developed by an Agency work
 group composed of scientists from
 throughout the Agency, and selected
 drafts were peer reviewed internally and
 by experts from universities,
 environmental groups, industry, and
 other governmental agencies. A
 subsequent draft has undergone peer
 review in a workshop held on June 2-
 3,1992, and has received internal
 review by the Concordance and
 Oversight Subcommittees of the Risk
 Assessment Ebrum. Most recently, the
 Committee od the Environment and
 Natural  Resources of,the Office of
 Science  and Technology Policy
 reviewed the guidelines at a meeting
 held on  August IS, 1995. The proposed
 Guidelines are based, in part, on
 recommendations derived from these
 reviews  and on those made at various
 scientific meetings and workshops on
 naurotoxicology.
  The public is invited to comment, and
public comments will be considered in
EPA decisions in formulating the final
Guidelines. Commenters are asked to
 focus on several special issues,
particularly, (1) the issue of
compensation and recovery of function
                     in neurotoxico logical studies and how
                     to account for compensation in
                     neurotoxicology risk assessment; (2) the
                     use of blood and/or brain
                     acetylcholinesterase activity as an
                     indication of neurotoxicity for risk •
                     assessment; (3) endpoints indicative of
                     neurotoxicity that may not be covered
                     by these guidelines, i.e., endocrine
                     disruption or neuroendocrine*mediated
                     neurotoxicity; and (4) the possibility of
                     no threshold for some neurotoxic
                     agents.
                       The EPA Science Advisory Board
                     (SAB) also will review these proposed
                     Guidelines at a meeting to be
                     announced in a future Federal Register.
                     Agency staff will prepare summaries of
                     the public and SAB comments, analyses
                     of major issues presented by
                     commenters, and Agency responses to
                     those comments. Appropriate comments
                     will be incorporated, and the revised
                     Guidelines will be submitted to the Risk
                     Assessment Forum for review. The
                     Agency will consider comments from
                     the public, the SAB. and the Risk
                     Assessment Forum in its
                     recommendations to the EPA
                     Administrator.
                     DATES: The Proposed Guidelines are
                     being made available for a 120-day
                     public review and comment period.
                     Comments must be in writing and must
                     be postmarked by February 1.1996.
                     Please submit one unbound original
                     with pages consecutively numbered.
                     and three copies. If there are
                     attachments, include an index
                     numbered coasecutively with
                     comments, and three copies.
                     FOR FURTHER INFORMATION CONTACT: Dr.
                    Hugh A. Tilson. Tel: 919-541-2671;
                    Fax: 919-541-4849.
                    ADDRESSES: Comments on the proposed
                    Guidelines may be mailed or delivered
                    to: Dr. Hugh A. Tilson. Neurotoxicology
                    Division (MD-74B), National Health and
                    Environmental Effects Research
                    Laboratory, U.S. Environmental
                    Protection Agency, Research Triangle
                    Park. NC 27711. Please note that all
                    comments received in response to this
                    notice will be placed in a public record.
                    Commenters should not send any item
                    of personal information, such as
                    medical information or home address, if
                    they do not wish it to be part of the
                    public record.
                    SUPPLEMENTARY INFORMATION: In its 1983
                    book. Risk Assessment in the Federal
                    Government: Managing the Process, the
                    National Academy of Sciences
                    recommended that Federal regulatory
                    agencies establish "inference
                    guidelines" (1) to promote consistency
                    and technical quality in risk assessment,
                    and' (2) to ensure that the risk
 assessment process is maintained as a
 scientific effort separate from risk
 management. A task force within EPA
 accepted that recommendation and
 requested that Agency scientists begin
 to develop such guidelines.
   In 1984, EPA scientists began work on
 risk assessment guidelines for
 carcinogenicity,.mutagenicity, suspect
 developmental toxicants, chemical
 mixtures, and exposure assessment.
 Following extensive scientific and
 public review, these first five guidelines
 were issued on September 24,1986 (51
 FR 33992-34054). Since 1986,
 additional risk assessment guidelines
 have been proposed for mole and female
 reproductive risk (53 FR 24834-847; 53
 FR 24850-869), and two of the 1986
 guidelines, suspect developmental
 toxicants (56 FR 63798-826) and
 exposure assessment (57 FR 22888-
 938}, have been revised, reproposed,
 and finalized.
   The Guidelines proposed today
 continue the guidelines development
 process initiated in 1984. These
 Guidelines set forth principles and
 procedures to guide EPA scientists in
 the conduct of Agency risk assessments
 and to inform Agency decision makers
 and the public about these procedures.
 In particular, the Guidelines emphasize
 that risk assessments will be conducted
 on a case-by-case basis, giving full
 consideration to all relevant scientific
 information. This case-by-case approach
 means that Agency experts study
 scientific information on each chemical
 under review and use the most
 scientifically appropriate interpretation
 t« assess risk. The Guidelines also stress
 that this information will be fully
 presented in Agency risk assessment
 documents, and that Agency scientists
 will identify the strengths and
 weaknesses of each assessment by
 describing uncertainties, assumptions,
 and limitations, as well as the scientific
basis and rationale for each assessment.
  The Guidelines are formulated in pan
to bridge gaps in risk assessment
methodology and data. By identifying
these gaps and the importance of the
missing information to the risk
assessment process. EPA wishes to
encourage research and analysis that
will lead to-new risk assessment
methods and data.
  Dated: September 25,199S.
Cirol M. Browner.
Administrator.
Propped Guideline* far Neorutoxicity  Risk
I. Introduction
 A. Organization of These Guidelines
 B. The Role of Environmental Agents in
   Neurotoxicity

-------
                     Federal  Register / Vol. 60.  No. 192 / Wednesday. October 4.  1995
     C. N'eurotoxicsty Riss Assessment
     D. Assumptions
   II. Definitions and Critical Concent?
   in. Hazard Characterization    P
     A. Neurotoxicological Studies: End Points
      and Their Interpretation
     1. Human Studies
     a. Clinical Evaluations
     b.- Case Reports
     c. Epidemiologic Studies
     (1) Cross-sectional studies
     (24 Case-control (retrospective) studies
     (3) Cohort (prospective, follow-up) studies
     d. Human Laboratory Exposure Studies
     2. Animal Studies
     a. Structural End Points of Neurotoxicity
     b. Neurophysiological End Point* of
      Neurotoxicity
     (1 j Nerve conduction studies
     (2) Sensory, motor, and other evoked
      potentials
    (3) Seizures/convulsions
    (4) Electroencephalography (EEC)
    c. Neurochemical End Points of
      Neurotoxicity
    d. Behavioral End Points of Neurotoxicity
    (1) Functional observational battery
    (2) Motor activity
 ,   (3) Schedule-controlled operant behavior
    (4) Convulsions
    (5) Specialized tests for neurotoxicity
    (a) Motor function
    (b) S«nsory function
    (c) Cognitive function .
    e. Developmental Neurotoxicity
    3. Other Considerations
    a. Pharmacokinetics
   b. Comparisons of Molecular Structure
   c. Statistical Considerations
   d. In Vitro Data in Neurotoxicology
 .  B. Dose-Response Evaluation
   C Characterization of the Health-Related
     DataBase
 IV. Dose-Response Analysis
   A. LOABL/NOAEL and Benchmark DOM
     (BMD) Determination
   B. Determination of the Reference Dose or
     Reference Concentration
 V. Exposure Assessment
 VI Risk Characterization
   A. Overview
   B. Integration of Hazard Characterization.
     Dose-Response Analysis, and Exposure
     Assessment
   C Quality of the Data Base and Degree of
     Confidence in the Assessment
   D. Descriptors of Neurotoxicity Risk
   1. Estimation of the Number of Individuals
   2. Presentation of Specific Scenarios
   3. Risk Characterization for Highly
     Exposed Individual*
   4. Risk Characterization for Highly
    Sensitive or Susceptible Individuals   •
   5. Other Risk Descriptor*
   E. Communicating Results
   F. Summary and Research Needs
vn. References

List of Table*
Table 1. Examples of possible indicators of a
    neurotoxic effect
Table 2. Neurotoxicant* and diseases with
    specific neuronal targets
Table 3. Examples of neurophysiological
    measures of neurotoxicity
Table 4. Examples of neurotoxicants with
    known neurochemical mechanisms
                                                                                                                 52033
   Table 5. Summary of measures in a
       representative functional observational
       battery, and the type of data produced bv
       each       ,  -                    *
   Table 6. Examples of specialized behavioral
       tests to measure neurotoxicity
   Table 7. Examples of developmental
       neurotoxicants
   Table 8. Characterization of the Health-   •
       Related Database
   I. Introduction
     These proposed Guidelines describe
   the principles, concepts, and procedures
   that the U.S. Environmental Protection
   Agency (EPA; Agency) would follow in
   evaluating data on potential
   neurotoxicity associated with exposure
   to environmental toxicants. The
   Agency's authority to regulate
   substances that have the potential to
   interfere with human health is derived
   from a number of statutes that are
   implemented through multiple offices
   within the EPA. The procedures
  outlined here are intended to help
  develop a sound scientific basis for
  neurotoxicity risk assessment, promote
  consistency in the Agency's assessment
  of toxic effects on the nervous system.
  and inform others of the approaches
  used by the Agency in those
  assessments.

  A. Organization of These Guidelines
    This Introduction (section I)
  summarizes the purpose of these
  proposed Guidelines within the overall
  framework of risk assessment at the
  EPA. It also outlines the organization of
  the guidance and describes several
  default assumptions to be used in the
  risk assessment process as discussed in
  the recent National Research Council
  report "Science and Judgment in Risk
 Assessment {NRC, 1994)."
   Section H sets forth definitions of
 particular terms widely used in the field
 of neurotoxicology. These include
 "neurotoxicity" and "behavioral
 alterations." Also included in this
 section are discussions concerning
 reversible and irreversible effects and
 direct versus indirect effects.
   Risk assessment is the process by
 which scientific judgments are made
 concerning the potential for toxicity to
 occur in humans. The National Research
 Council (NRC. 1983) has defined risk
 assessment as including some or all of
 the following components (paradigm):
 hazard identification, dose-response
 assessment, exposure assessment, and
 nsk characterization, to its 1994 report
 "Science and Judgment in Risk
Assessment" the NRC extended its view
of the paradigm to include
characterization of each component
(NRC 1994). In addition, it noted the
importance of an approach that is less
    fragmented and more holistic, less
    linear and more interactive, and one
    that deals with recurring conceptual
    issues that cut across all stages of risk
    assessment. These Guidelines prooose a
    more interactive approach by organizing
    the process around components that
    focus on evaluation of the toxicity data
    (hazard characterization), the
    quantitative dose-response analysis the
    exposure assessment, and the risk
   characterization. This is done because,
   in practice, hazard identification for
   tteurotoxicity and other noncancer
   health effects is usually done in
   conjunction with an evaluation of dose-
   response relationships in the studies
   used to identify the hazard.  Determining
   a hazard often depends on whether a
   dose-response relationship is present
   (Kunmel et al.. 1990). Thus,  the hazard
   characterization provides an evaluation
   of a hazard within the context of the
   dose, route, duration, and timing of
   exposure. This approach combines the
   information important in comparing the
   toxicity of a chemical to potential
   human exposure scenarios (Section V)
  Secondly, it avoids the potential for
   labeling chemicals as "neurotoxicants"
  on a purely qualitative basis. This
  organization of the risk assessment
  process is similar to that discussed in
  the Guidelines for Developmental
  Toxiriry Risk Assessment (56 FR
  63798), the main difference being that
  the quantitative dose-response analysis
  is discussed under a separate section in
  these guidelines.
    Hazard characterization involves
  examining all available experimental
  animal and human data and the
  associated doses, routes, timing, and    '
  durations of exposure to determine if an
  agent causes neurotoxicity in that
  species and under what conditions.
  From the hazard characterization and
 criteria provided in these Guidelines,
 the health-related data base can be
 characterized as sufficient or
 insufficient for use in risk assessment
 (section m.C). Combining hazard
 identification and some aspects of dose-
 response evaluation into hazard
 characterization does not preclude the
 evaluation and use of data when
 quantitative information for setting
 reference doses (RfDs) and reference
 concentrations (RfCs) are not available.
   The next step, the dose-response
 analysis (section IV) is the quantitative
 analysis, and includes determining the
 no-observed-adverse-effect-level
 (NQAEL) and/or the lowest-observed-
 adverse-effect-level (LOAEL) for each
 study and type of effect. Because of the
 limitations associated with the use of
 the NOAEL, the Agency is beginning to
use an additional approach, i.e., the

-------
52034
Federal  Register '  Vol. 60, No. 192 / Wednesday. October 4, 1995  / Notices
Benchmark dose approach (Crump,
1984: U.S. EPA. 1995a). for more
quantitative dose-response evaluation
when sufficient data are available. The
benchmark dose approach takes into-
account the variability in  the data and
the slope of the dose-response curve,
and provides a more consistent basis for
calculation of the RfD or RfC. If data are
considered sufficient for risk
assessment, and if neurotoxicity is the
effect occurring at the lowest dose level
(i.e.. the critical effect), an oral or
dermal RfD or an inhalation RfC, based
on neurotoxic effects, is then derived.
This RfD or RfC is derived using the
NOAEL or benchmark dose divided by
uncertainty factors to account for
interspecies differences in response,
intraspecies variability and other factor >.
of study design or the data base. A.
statement of the potential for human
risk and the consequences of exposure
can come only from integrating the
hazard characterization and dose-
response analysis with the human
exposure estimates in the final risk
characterization.     *
  The section on exposure assessment
(section V) identifies human
populations exposed or potentially
exposed to an agent, describes their
composition and size, and presents the
types, magnitudes, frequencies, and
durations of exposure to the agent; The
exposure assessment provides an
estimate of human exposure levels for
particular populations from all potential
sources.
  In risk characterization (section VI).
the hazard characterization, dose-
response analysis, and the exposure
assessment for given populations are
combined to estimate some measure of
the risk for neurotoxicity. As part of risk
characterization, a summary of the
strengths and weaknesses of each
component of the risk assessment is
given along with major assumptions,
scientific judgments, and. to the extent
possible, qualitative and quantitative
estimates of the uncertainties. This
characterization of the health-related
data bast, is always presented in
conjunction with information on the
dose, route, duration and timing of
exposure as well as the dose-response.
analysis including the RfD or RfC If
human exposure estimates are available,
the exposure basis used for the risk
assessment is clearly described, e.g., .
highly exposed individuals or highly
sensitive or susceptible individuals. The
NOAEL may be compared to the various
estimates of human exposure to
calculate the margin(s) of exposure
(MOE). The considerations for judging
the acceptability of the MOE are similar
to those for determining the appropriate
                      size of the uncertainty factor for
                      calculating the RfD or RfC.
                        The Agency recently issued a policy
                      statement and associated guidance for
                      risk characterization (U.S. EPA. 1995b.
                      I995c), which is currently being
                      implemented throughout EPA. This
                      policy statement is designed to ensure
                      that critical information from each stage
                      of a risk assessment is used in forming
                      conclusions about risk and that this
                      information is communicated from risk
                      assessors- to risk managers (policy
                      makers), from middle to upper
                      management, and from the Agency to
                      the public. Additionally, the policy
                      provides a basis for greater clarity,
                      transparency, reasonableness, and
                      consistency in risk assessments across
                      Agency programs. Final neurotoxicity
                      risk assessment guidelines may reflect
                      additional changes in risk
                      characterization practices resulting from
                      implementation activities.
                        Risk assessment is just one
                      component of the regulatory process
                      and defines the potential adverse health
                      consequences of exposure to a toxic
                      agent. The other component risk
                      management, combines risk assessment
                      with statutory directives regarding
                      socioeconomic, technical, political, and
                      other considerations, to decide whether
                      to control future exposure to the
                      suspected toxic agent and, if so. the
                      nature and level of control. One major
                      objective of these risk assessment
                      Guidelines is to help the risk assessor
                      determine whether the experimental
                      animal or human data indicate the
                      potential for a neurotoxic effect Such.
                      information can then be used
                      subsequently to categorize evidence to
                      identify and characterize neurotoxic
                      hazards as described in section OL3.C.
                      Characterization of the Health-Related
                      Data Base, and Table 8 of these
                      Guidelines. Risk management is not   ,
                      dealt with directly in these Guidelines
                      because the basis for decision making
                      goes beyond scientific considerations
                      alone, but the use of scientific
                      information in this process is discussed.
                      For example, the acceptability of the
                      MOE is a risk management decision, but
                      the scientific bases for establishing this
                      value are discussed here.
                      B. The Role of Environmental Agents in
                      Neurotoxicity  .
                        Chemicals are an integral part of life.
                      with the capacity to improve as well as
                      endanger health.  The general population
                      is exposed to chemicals with neurotoxic
                      properties in air.  water, foods,
                      cosmetics, household products, and
                      drugs used therapeutically or illicitly.
                      Naturally occurring neurotoxins. such
                      as animal and plant toxins, present
additional hazards. During daily life, a
person experiences a multitude of
exposures, both voluntary and
unintentional, to neuroactive
substances, singly and in combination.
Levels of exposure vary and may or may
not pose a hazard depending on dose.
route, and duration of exposure.
  A link between human exposure to
some chemical substances and'
neurotoxicity has been firmly
established (Anger, 1986; OTA, 1990).
Because many natural and synthetic
chemicals are present in today's
environment, there is growing scientific
and regulatory interest in the potential
for risks to humans from  exposure to #
neurotoxic agents. If sufficient exposure
occurs, the effects resulting from such
exposures can have a  significant adverse
impact on human  health. It is not
known how many chemicals may be
neurotoxic in humans (Reiter, 1987).
The EPA's inventory of toxic chemicals
is greater than 63,000 and increasing
yearly. An overwhelming majority of the
materials in commercial use have not
been tested for their neurotoxic
potential (NRC, 1984). Estimates of the
number of chemicals  with neurotoxic
properties have been made for subsets of
substances. For instance, a large
percentage of the more than 500
registered active pesticide ingredients
are neurotoxic to varying degrees. Of
588 chemicals listed by the American
Conference of Governmental Industrial
Hygienists. 167 affected the nervous
system or behavior at  some exposure
level (Anger, 1984). Anger (1990)
estimated that of the approximately 200
chemicals to which one million or more
American workers are exposed, more
than one-third may have adverse effects
on the nervous system, if sufficient
exposure occurs. Anger (1984) also
recognized neurotoxic effects as one of
the 10 leading workplace disorders. A
number of therapeutic substances,
including some anticancer and antiviral
agents and abused drugs, can cause
adverse or neurotoxicological side
effects at therapeutic levels (OTA.
1990). Thus, estimating the risks of
exposure to chemicals with neurotoxic
pptential is of concern with regard to
the overall impact of these exposures on
human health.

C. Neurotoxicity Risk Assessment
  In addition to its primary role in
cognitive functions, the nervous system
controls most, if not all. other bodily
processes. It is sensitive to perturbation
from various sources and has limited
ability to regenerate. There is evidence
that even small anatomical,
biochemical, or physiological insults to
the nervous system may result in

-------
                 Federal  Register  /  Vol. 60. N'o.  192 / Wednesday. October  4.  1995 / Nonces
                                                                    52035
adverse effects on human health.
Therefore, there is a need for consistent
guidance on how to evaluate data on
neurotoxic substances and assess to
what degree, if any, they have the
potential to cause transient or
persistent, direct or indirect effects on
human health.
  To help address these needs, these
Guidelines develop principles and
concepts in several areas. First, these
Guidelines outline the scientific  basis
for evaluating effects due to exposure to
neurotoxicants and discuss principles
and methods for evaluating data  from
human and animal studies on behavior,
neurochemistry. neurophysiology, and
neuropathology. This guidance
document also discusses adverse effects
on neurological development and
function in infants" and children
following prenatal and perinatal
exposure to chemical agents. Other
sections of these Guidelines outline the
method for calculating reference doses
or reference concentrations when
neurotoxicity is the critical effect.
discuss the availability of alternative
mathematical approaches to dose-
response analyses, characterize the
health-related data base for
neurotoxicity risk assessment, and
discuss integration of exposure
information with the results of the dose-
response assessment to characterize
risks of exposures of concern. These
Guidelines do not advocate developing
reference doses specific for
neurotoxicity. but rather the use  of
neurotoxicity as one possible end point
to develop reference doses.
  EPA offices have published guidelines
for neurotoxicity testing in animals
(U.S. EPA. 1986.1987,1988af 1991a).
The testing guidelines address the
development of new data for us* in risk
assessment. These proposed
neurotoxicity risk assessment
Guidelines provide the Agency's first
comprehensive guidance on the use and
interpretation of neurotoxicity data.
These proposed Guidelines are part of
the Agency's risk assessment guidelines
development process, which was
initiated in 1984. As part of its
neurotoxicity guidelines development
program, the EPA has sponsored or
participated in several conferences on
relevant issues (Tilson. 1990); these and
other sources (see references) provide
the scientific basis for these proposed
risk assessment Guidelines. This
guidance is intended for use by Agency
risk assessors and is separate and
distinct from the recently published
document on principles of neurotoxicity
risk assessment (U.S. EPA. 1993). The
document on principles was prepared
under the auspices of the Subcommittee
 on Risk Assessment of the Federal
 Coordinating CSonal for Science,
 Engineering, and Technology and was
 not intended to provide specific
 directives for how neurotoxicity risk
 assessment should be performed.
   It is expected that, like other EPA risk
 assessment guidelines (U.S. EPA,
 199lb), this document will encourage
 research and analysis leading to new
 risk assessment methods and data,
 which in turn would be used to revise
 and improve the Guidelines and better
 guide Agency risk assessors.
 D. Assumptions
  There are a number of unknowns in
 the extrapolation of data from animal
 studies to humans. Therefore, a number
 of default assumptions are made that are
 generally applied in the absence of data
 on the relevance of effects to potential
 human risk. Default assumptions should
 not be applied indiscriminantly. First.
 all available mechanistic and
 pharmacokinetic data should be
 considered.  If these data indicate that an
 alternative assumption is appropriate or
 obviate the need for applying an
 assumption, such information should be
 used in the risk assessment of that
 agent The following default
 assumptions form the basis of the
 approaches taken in these Guidelines.
  It is assumed that an agent that
 produces detectable adverse neurotoxic
 effects in experimental animal studies
 will pose a potential hazard to humans.
 This assumption is based on the
 comparisons of data for known human
 neurotoxicants (Anger. 1990; Kimmel et
 al., 1990: Spencer and Schaumburg,
 1980). which indicate that experimental
 animal data are frequently predictive of
 a neurotoxic effect in humans.
  It is assumed that behavioral,
 neurophysiological, neurochemical. and
 neuroanatomical manifestations are of
 concern. In the past, the tendency has
been to consider only neuropathological
 changes as end points of concern. Based
 on the data on agents that are known  .
 human neurotoxicants (Anger, 1990;
 Kimmel et aL, 1990; Spencer and
 Schaumberg. 1980), there is usually at
 least one experimental species that
 mimics the types of effects seen in
 humans, but in other species tested, the
type of neurotoxic effect may be
different or absent Thus, a biologically
significant increase in any of the   • •
manifestations is considered indicative
of an agent's potential for disrupting the
structure or function of the human
 nervous system.
  It is assumed that the types of
 neurotoxic effects seen in animal
 studies may not always be the same as
 those produced in humans. Therefore, it
 may be difficult to determine which will
 be the most appropriate species in terms
 of predicting the specific types of effects
 seen in humans. The fact that every
 species may not react in the same way
 is probably due to species-specific
 differences in maturation of the nervous
 system, differences in timing of
 exposure, metabolism, or mechanisms
 of action.
   It is assumed that the most
 appropriate species will be used when
 data are available to estimate human
 risk. In the absence of such data, the
 most sensitive species is used, based on
 the fact that for the majority of known
 human neurotoxicants, humans are as
 sensitive or more so than the most r
 sensitive animal species tested.    /
   In general, a threshold is assumed for
 the dose-response curva for most
 neurotoxicants. This is based on the
 known capacity of the. nervous-system
 to compensate for or to repair a certain
 amount of damage at the cellular, tissue.
 or organ level. In addition, because of
 the multiplicity of cells in the nervous
 system, multiple insults at the
 molecular or cellular level may be
 required to produce an effect on the
 whole organism.
  These assumptions are "plausibly
 conservative"  (NRC, 1994) in that they
 are protective of public health and are
 also well-founded in scientific
 knowledge about the effects of concern.

 n. Definitions and Critical Concepts
  This section defines the key terms aud
 concepts that the EPA will use in the
 identification and evaluation of
 neurotoxicity.  The various health effects
 that fall within the broad classification
 of neurotoxicity are described and
 examples are provided.
  Adverse effects include alterations
 from baseline that diminish an
 organism's ability to survive, reproduce.
 or adapt to the environment.
 Neurotoxicity is an adverse change in
 the structure or function of the central
 and/or peripheral nervous system
 following exposure to a chemical.
 physical, or biological agent (Tilson.
 1990). Neurotoxic effects include
 changes in somatic/autonomic. sensory,
 motor, and/or cognitive function.
 Structural effects are defined as
 neuroanatomical changes occurring at
 any level of nervous system
 organization; functional changes are
 defined as neurochemical.
 neurophysiological. or behavioral
 alterations. Changes in function can also
.result from toxicity tq other specific
 organ systems, and these indirect
 changes may be considered adverse but
 not necessarily neurotoxic.

-------
52036
Federal  Register   Vol. 60, No.  192 / Wednesday, October 4.  1995 / Notices
  The nsk assessor also should know
that there are different levels of concern
based on the magnitude of effect and
reversibility of some neurotoxic effects.
Neuiotoxic effects may be irreversible,
i.e., cannot return to the state prior to
exposure, resulting in a permanent
change in. the organism, or reversible,
i.e., can return to the pre-exposure
condition, allowing the organism to
return to its state prior to exposure.
Clear or demonstrable irreversible
change in either the structure or
function of the nervous system causes
greater concern than do reversible
changes. If neurotoxic effects are
observed at some time during the life
span of the organism but are slowly
reversible, the concern is also high.
There is lesser concern for effects that
are rapidly reversible or transient, i.e.,
measured in minutes, hours, or days,
and appear to be associated with the
pharmacokinetics of the causal agent
and its presence in the body. Reversible
changes that occur in the occupational
setting or environment, however, may
be of high concern if, for example,
exposure to a short-acting solvent
interferes with operation of heavy
equipment in an industrial plant The
context of the exposure should be
considered in evaluating reversible
effects. The risk assessor should note
that once damaged, neurons,
particularly in the central nervous
system, have a limited capacity for
regeneration. Reversibility of effects
resulting from cell death or from the
destruction of cell processes may
represent an activation of repair
capacity, decreasing future potential
adaptability. Therefore, even reversible
r.eurotoxic changes should be of
concern. Evidence of progressive effects,
i.e..  those that continue to worsen even
after the causal agent has been removed;
or delayed effects, i.e., those that occur
at a time distant from the last contact
with the causal agent; or residual
effects, i.e., those that persist beyond a
recovery period: or latent offsets, i.e.,
those that become evident only after an
environmental challenge or aging, have
a high level of concern. Environmental
challenges can include stress, increased
physical or cognitive workload.
pharmacological manipulations, and
nutritional deficiency or excess.
   Neurotoxic effects can be observed at
various levels of organization of the
nervous system, including
neurochemicaJ, anatomical,
physiological, or behavioral. At the
neurochemical level, for example, an'
agent that causes neurotoxicity might
inhibit rnacromolecule or transmitter
synthesis, alter the flow of ions across
                      cellular membranes, or prevent release
                      of neurotransmitter from the nerve
                      terminals. Anatomical changes may
                      include alterations of the cell body, the
                      axon. or the myelin sheath. At the
                      physiological level, a chemical might
                      change the thresholds for neural
                      activation or reduce the speed of
                      neurotransmission. Behavioral
                      alterations can include significant
                      changes in sensations of sight, hearing,
                      or touch; alterations in simple or
                      complex reflexes and motor functions;
                      alterations in cognitive functions such
                      as learning, memory or attention; and
                      changes in mood, such as fear or rage,
                      disorientation as to person, time, or
                      place, or distortions of thinking and
                      feeling, such as delusions and
                      hallucinations. At present, relatively
                      few neurotoxic syndromes have been
                      thoroughly characterized in terms of the
                      initial neurochemical change, structural
                      alterations, physiological consequence,
                      and behavioral effects. Knowledge of
                      exact mechanisms of action is not.
                      however, necessary to conclude that a
                      chemically induced change is a
                      neurotoxic effect,
                        Neurotoxic effects can be produced by
                      chemicals that do not require
                      metabolism prior to interacting with
                      their target sites in the nervous system,
                      i.e.. primary neurotoxic agents, or those
                      that require metabolism prior to
                      interacting with their target sites in the
                      nervous system, i.e., secondary
                      neurotoxic agents. Chemically induced
                      neurotoxic effects can be direct, i.e., due
                      to an agent or its metabolites acting
                      directly on target sites in the nervous
                      system, or indirect, i.e., due to agents or
                      metabolites that produce their effects
                      primarily by interacting with target sites
                      outside the nervous system, which
                      subsequently affect target sites in the
                      nervous system. Excitatory amino acids
                      such as domoic add damage specific
                      neurons directly by activating excitatory
                      amino acid receptors in the nervous
                      system, while carbon monoxide
                      decreases oxygen availability, which
                      indirectly kills neurons. Other examples
                      of indirect effects of chemicals that
                      could lead to altered structure and/or
                      function of the nervous system include
                      cadmium-induced spasms in blood
                      vessels supplying the nervous system.
                      dichloroacetate-induced perturbation of
                      metabolic pathways, and chemically
                      induced alterations in skeletomuscular
                      function or structure and effects on the
                      endocrine system. Professional
                      judgment may be required in making
                      determinations about direct versus
                      indirect effects.
                        The interpretation of data as
                      indicative of a 'potential neurotoxic
                      effect involves the evaluation of the
validity of the data base. This approach
and these terms have been adapted from
the literature on human psychological
testing (Sette, 1987; Sette and MacPhail,
1992) where they have long been used
to evaluate the level of confidence in
different measures of intelligence or
other abilities, aptitudes, or feelings.
There are four principal questions that
should be addressed: whether the effects
result from exposure (content validity);
whether the effects are adverse or
toxicologicaily significant (construct
validity); whether there are correlative
measures among behavioral,
physiological, neurochemical, and
morphological end points (concurrent  j
validity); and whether the effects are  a
predictive of what will happen under '•/
various conditions (predictive validity).
Addressing these issues can provide a
useful framework for evaluating either
human or animal studies or the weight
of evidence for a chemical (Sette, 1987;
Sette and MacPhail, 1992). The next
sections indicate the extent to which
chemically  induced changes can be
interpreted  as providing evidence of
neurotoxicity.

m. Hazard Characterization

A. Neurotoxicological Studies: End
Points and  Their Interpretation
  Identification and characterization of
neurotoxic hazard can be based on
either human or animal data (Anger,
1984; Reiter, 1987; U.S. EPA. 1993).
Such data can result from accidental,
inappropriate, or controlled
experimental exposures. This section
describes many of the general and some
of the specific characteristics of human
studies and reports of neurotoxicity. It
then describes some features of animal
studies of neuroanatomical.
neurochemical, neurophysiological. and
behavioral effects relevant to risk
assessment The process of
characterizing the sufficiency or
insufficiency of neurotoxic effects for
risk assessment is described in section
m.C Additional sources of information
relevant to hazard characterization, such
as comparisons of molecular structure
among compounds and in vitro
screening methods, are also discussed.
  The hazard characterization should:
  a. Identify strengths and limitations of
the database:
•^-Epidemiological studies (case reports,
  cross-sectional, case-control, cohort.
  or human laboratory exposure
  studies);
—Animal studies including (structural
  or neuropathological, deurochemical,
  neurophysiological, behavioral or
•  neurological, or developmental end
  points).

-------
                 Federai  Register    V0[. 60. N'Q.  192 / Wednesday. Qctooer 4. 1995  /  Notices
                                                                     32037
   b. Evaluate die vilicity of ihe
 database:
 —Content validity (effects result from
   exposure):
 —Construct validity (effects are adverse
   or toxico logically- significant);
 —Concurrent validity (correlative
   measures among behavioral,
   physiological, neurochemical, or
   morphological end points);
—Predictive validity (effects are-
  predictive of what will happen under
  various conditions).
  c. Identify and describe key
lexicological studies.
  d. Describe the type of effects:
—Structural fneuroanatomical
•  alternations);
—Functional (neurochemicar,
  neurophysiological. behavioral
  alterations).
  e. Describe the nature of the effects
(irreversible, reversible, transient,
progressive, delayed, residual, or latent
effects).
  f. Describe how. much  is known about
how (through what biological
mechanism) the chemical produces
adverse effects.
  g. Discuss other health end points of
concern.
  h. Comment on any non-positive data
in humans or animals.
  i. Discuss the dose-response data
(epidemiological qr animal) available for
further dose-response analysis.
  j. Discuss the route, level, timing, and.'
duration of exposure in studies '
demonstrating neurotoxicity as '
compared to expected human   "
exposures.
  k. Summarize the hazard
characterization:
—Confidence in conclusions;.
—Alternative conclusions also
  supported by the data;
—Significant data gaps; and
—Highlight of major assumptions.

1. Human Studies
  It is well established that information
from the evaluation of human exposure
can identify neurotoxic hazards (Anger
and Johnson, 1985; Anger. 199O).
Prominent among historical episodes of
neurotoxicity in human.populations are
the outbreaks of methylmercury
poisoning in Japan and Iraq and the
neurotoxicity seen in miners of metals,
including mercury, manganese, and lead
(Carson et al.. 1987; Silbergeld and
Percival. 1987; OTA. 1990). In the last
decade, lead poisoning in children has '
been a prominent issue of concern
(Silbergeld and Percival.  1987).
Neurotoxicity in humans has been
studied and reviewed for many
pesticides (Hayes, 1982; NRDC, 1989:
 Ecobichon and Joy, 1982; Ecobichon et
 al., 1990). Organochlorines,
 organophosphates, 'carbamates,^
 pyrethroids. ceriSba fungicidesV'and
 some fumigants ;are all- known
 neurof oxicants. They may pose
 occupational risks to manufacturing and
 formulation, workers, pesticide
 applicators and farm workers, and
 consumers through home application or
 consumption of residues in foods.
 Families of workers may also be
 exposed by transport into the home
 from workers' clothing. Data on humans
 can come from a number of sources,
 including rUnirat evaluations, case
 reports, and epidemiologic studies. A
 more extensive description of issues
 concerning human neurotoxicology and
 risk assessment has been published
 elsewhere (U.S. EPA. 1993).
   a. Clinical Evaluations. Clinical
 methods are used extensively in
 neurology and neuropsychology to
 evaluate patients suspected of having
 neurotoxicity. An extensive array of
 examiner-administered and paper-and-
 pencil tasks are used to assess sensory,
 motor,, cognitive, and affective functions
 and personality states/traits.
 Neurobehavioral data are synthesized
 with information from neurophysiologic
 studies and medical history to derive a
 working diagnosis. Brain imaging''
 techniques based on magnetic resonance
 imaging or  emission tomography may
 also be useful in helping, diagnose
 neurodegenerative disorders following
 chemical exposures in humans (Omerod
 et al., 1994; Callender et al., 1994).
 Clinical diagnostic approaches have
 provided a  rich conceptual framework
 for understanding the functions (and
 malfunctions) of the central and
 peripheral nervous systems and have
 formed the  basis for die development of
 methods for measuring the behavioral
 expression  of nervous system disorders.
 Human neurobehaviorai toxicology has
 borrowed heavily from neurology and
 neuropsychology for concepts of
 nervous system impairment and
 functional assessment methods.
 Neurobehavioral toxicology has adopted
 the neurologic/neuropsycnologic model,
 using adverse changes in behavioral
 function to  assist in identifying
 chemically or drug-induced changes in
 nervous system processes.
  Neurologic and neuropsychologic
 methods have long been employed to
 identify the adverse health effects of
 environmental workplace exposures
 (Sterman and Schaumburg. 1980).
Peripheral neuropathies-(with sensory
and motor disturbances),
encephalopathies, organic brain
syndromes, extrapyramidal syndromes.
demyelination, autonomic changes, and
 dementia are well-characterized
 consequences of acute and chronic
 exposure to chemical agents. The range
 of exposure conditions that produce
 clinical signs of neurotoxicity also has
 been defined by these clinical methods.
 It is very important to make external/
 internal dose measurements in humans
 to determine the actual dose(s) that can
 cause unwanted effects.
   Aspects of the neurologic examination
 approach limit its usefulness for
 neurotoxicologicrisk assessment.
 Information obtained from the*
 neurologic exam is mostly qualitative
 and descriptive rather than quantitative.
 Estimates of the severity of functional
 impairment can be reliably placed intrf
 only three or four categories (for    J
 example, mild, moderate, severe). Much
 of the assessment depends on the
 subjective judgment of the examiner. •
 For example, the magnitude and
 symmetry of muscle strength  are o ften
 judged by having the patient push
 against the resistance of the examiner's1
 hands. The end points are therefore the
 absolute and relative amount of muscle
 load sensed by the examiner in his or
 her arms.
   Compared with other methods, the
 neurologic exam may be  less sensitive
 in detecting early neurotoxicity in
 peripheral sensory and motor nerves."'
 While clinicians' judgments are equal in
 sensitivity to quantitative methods in
 assessing the amplitude of tremor,
 tremor frequency is poorly quantified by
 clinicians. Thus, important aspects of
 the clinical neurologic exam may be
 insufficiently quantified and lack
 sufficient sensitivity for detecting early
 neurobehaviorai toxicity  produced by
 environmental 'or workplace exposure
 conditions. However, a neurologic
 evaluation of persons with documented
 neurobehaviorai impairment would be
 helpful for identifying nonchemical
 causes of neurotoxicity, such as diabetes
 and cardiovascular insufficiency.
  Administration of a
 neuropsychological battery also requires
 a trained technician, and  interpretation
 requires a trained and experienced
 neuropsychologist Depending on the
 capabilities of the patient, 2 to 4 hours
 may be needed to administer a full
 battery; 1 hour may be needed for the
 shorter screening versions. These
 practical considerations may limit the
 usefulness of neuropsychological
assessment in large field studies of
suspected neurotoxicity.
  In addition to logistical problems in
administration and interpretation.
neuropsychological batteries and
neurologic exams share'two
disadvantages with respect to
neurotoxicity risk assessment. First,

-------
 52C38	Federal Register / Vol. 60. N'o. 192  /  Wednesday.  October 4. 1995  ,  Notices
neurologic exams and
neuropsychological test batteries are
designed to confirm and classify
functional problems in individuals
selected on the basis of signs and
symptoms identified by the patient.
family, or other health professionals.
Their usefulness in detecting low base-
rate impairment in workers or the
general population is generally thought
to be limited, decreasing the usefulness
of clinical assessment approaches for
epidemiologic risk assessment
  Second, neurologic exams and
neuropsychologic test batteries were
developed to assess the functional
correlates of the most common forms of
nervous system dysfunction: brain
trauma, focal lesions, and degenerative
conditions. The rfiniral tests were
validated against these neurologic
disease state*. With a few notable
exceptions, rh«mir»l« are not believed
to produce impairment similar to that
from trauma or lesions; nsurotoxic
effects are more similar to the effects of
degenerative disease. There Has been.
insufficient research to demonstrate
which tests designed to assess
functional expression of neurologic
disease are useful in characterizing the
modes of central nervous system
impairment produced by chemical
agents and drugs.
  b. Case reports. The first type of
human data available is often the case
report or case eeries, which can identify
cases of a disease and are reported by
clinicians or discerned through active or
passive surveillance, usually in the
workplace. However, case reports where
exposure involved, a single neurotoxic
agent, although informative, are rare in
the literature: for example, fanners an
likely to be-exnoeed to a wide variety of
potentially neurotoxic pesticide*.  .
Careful case histories assist in
identifying common risk factors.
especially when the association between
tha exposure and disease is strong, the
mode of action of tha agent is
biologically plausible, and clusters.
occur in a limited period of time.
  Case reports are inexpensive
compared with epidemiologic studies
and can be obtained more quickly than
more complex studies. However, they
provide little information about disease
frequency or population at risk, but
their importance has been dearly
demonstrated, particularly in accidental
poisoning or acute exposure to high
levels of toxicant They remain an
important source of index cases of new
diseases and for surveillance.
  a Epidemiologic Studies.
Epidemiology has been defined as "the
study of the distributions and
determinants of disease and injuries in
 human populations" [Mausner and
 Kramer. 1985). Knowing the frequency
 of illness in groups and the factors that
 influence the distribution is the tool of
 epidemiology that allows the evaluation
 of causal inference with the goal of
 prevention and cure of disease
 (Friedlander and Hearn, 1980),
 Epidemiologic studies are a means of
 evaluating the effects of neurotoxic
 substances on human populations, but
 such studies are limited because they
 must be performed shortly alter
 exposure if the effect is acute. Most
 often these effects an suspected to be a
 result of occupational exposures due to
 tha increased opportunity for exposure
 to industrial and other chemicals.
 Frequently, determining the precise
 dose or exposure concentration can be
 difficult in epidemiological studies.
  (1) Cross-sectional studies. In cross-
 sectional studies or surveys, both the
 disease and suspected risk factors an
 ascertained at the same time, and the
 findings are useful in generating
 hypotheses. A group of people an
 interviewed, examined, and tested at a
 single point in H<»K» to ascertain a
 relationship between a Himae* and a
 neurotoxic exposure. This study design
 does not allow the investigator to
 determine whether the disease or the
 exposure came first, rendering it less
 useful in estimating risk. These studies
 are. intermediate in cost and time
 required to complete compared with
 case reports and man complex
 analytical studies but should b*
 augmented with additional data.
  (2) Case-control (retrospective)
 studies. Last (1986} defines a case-
 control study as one that "starts with
 the identification of persons with the
 disease (or other outcome variable) of
 interest, and a suitable control
 population (comparison, reference
 group) of persons without the disease."
 He states that the relationship of an
 "attribute!* to the disease is measured by
 comparing the diseased with the
 nondiseased with regard to how
 frequently the attribute is present in
 each of the groups. The cases an
 assembled from a population of persons
 with and without exposure, and the
 comparison group is selected, from the
 same population; the relative
 distribution of the potential risk factor
 (exposure) in both groups is evaluated
by computing an odds ratio that serves.
as an estimate of the strength of the
association between the disease and the
 potential risk factor. The statistical
significance of the ratio is determined
by calculating a p-value and is used to
approximate relative risk.
  The case-control approach to the
study of potential neurotoxicants in the
 environment provides a great deal of
 useful information for the risk assessor.
 In his textbook, Valciukas (1991) notes
 that the case-control approach is the
 strategy of choice when no other
 environmental or biological indicator of
 neurotoxic exposure is available. He
 further states: "Considering the fact that
 for the vast majority of neurotoxic
 chemical compounds, no objective
 biological indicators of exposure are
 available (or if they are. their half-Hfe is
 too short to be of any practical value),
 the case-control paradigm is a widely
 accepted strategy for the assessment of
 toxic causation." Tha case-control study
 design, however, can be very      t
 susceptible to bias. The potential   f
 sources of bias are numerous and can be
 specific to a particular study. Many of
 these biases also can be present in cross-
 sectional studies. For example, recall
 bias or faulty recall of information by
 study subjects ia a questionnaire-based
 study caa distort the results of the
 study. Analysis of tha case-comparison
 study design assumes that the selected
 cases are representative persons with
 the disease—either all cases with the
 disease or a representative sample of
 them have been ascertained. It further
 assnme« that the control or comparison
 group is representative of the
 nondiseased population (or that the
 prevalence of the characteristic under
 study is the same in the control group
 as ia the general population). Failure to
 satisfy these assumptions may result in
 selection bias, but violation of
 assumptions does not necessarily
 invalidate the study results.
  An additional source of bias in case-
 control studies is the presence of
 confounding variables, i.e., factors
 known to be associated with the
 exposure and causally related to the
disease under study. These must be  .
 controlled either in the design of the
 study by matching cases to controls on
 the basis of the confounding factor or in
 the analysis of the data by using
 statistical techniques such as
 stratification or regression. Matching
requires time to identify an adequate
 number of potential controls to
 distinguish those with the proper
characteristics, while statistical control
of confounding factors requires a larger
study.
  The definition of exposure is critical
 in epidemiologic studies. In
occupational settings, exposure
assessment often is based on th.e job
assignment of the study subjects, but
can be more precise if detailed company
records allow the development of
exposure profiles. Positive results  from
a properly controlled retrospective

-------
Federal  Register-/ Vol. 60, N'o«  192.'  Wednesday.  Octoger
                                                                                                           52t)39
study should-wei§h heavily in the risk
assessment process.
  (3) Cohort (prospective, followup)
studies. In a prospective study design, a
healdiy group of people is assembled
and followed forward in time and
observed for the development of
disease. Such studies are invaluable for
determining the time course for
development of disease (e.g., followup
studies performed in. various cities on
the effects of lead on child
development). This approach allows the
direct estimate of risks attributed to a
particular exposure since disease
incidence rates in the cohort can be
determined. Prospective study designs
also allow die study of chronic effects
of exposure. One major strength of the
cohort design is that it allows the
calculation of rates to determine the
excess risk associated with an exposure.
Also, biases are reduced by obtaining
information before the disease develops.
This approach, however, can be very
time-consuming and costly.
  In cohort studies information bias can
be introduced when individuals provide
distorted information about their health
because they know their exposure status
and may have been told of the expected
health effects of the exposure under
study.
  A special type of cohort study is the
retrospective cohort study in which the
investigator goes back in time to select
the study groups and traces them over
time, often to the present. The studies
usually involve specially exposed
groups and have provided much
assistance in estimating risks due to
occupational exposures. Occupational
retrospective cohort studies rely on
company records of past and current
employees that include information on
the dates of employment, age at
employment, date of departure, and
whether diseased (or dead in the case of
mortality studies). Workers can then be
classified by duration and degree of
exposure. Positive results from a
properly controlled prospective study-
should weigh heavily in the risk
assessment process;
  d. Human Laboratory Exposure
Studies. Neurotoxicity assessment has
an advantage not afforded the
evaluation of other toxic end points,
such as cancer or reproductive toxicity,
in that the effects of some chemicals are
short in duration and reversible. This
makes it ethically possible to perform
human laboratory exposure studies and
obtain data relevant to the risk
assessment process.. Information from
experimental human exposure studies
has been used to set occupational
exposure limits, mostly for organic
solvents that can be inhaled. Laboratory
                      exposure studies have contributed to
                      risk assessment,arid the setting of
                      exposure- liniffl for'several solvents and
                      other chemicals'with acute reversible
                      effects.        -'''•  -   " '   .
                        Human exposure studies sometime
                      offer advantages over epidemiologic
                      field studies. Combined with "^
                      appropriate sampling-of biologic fhiids
                      (urine or blood), it is possible to ••'<•-• - •
                      calculate-body concentrations-, exantine
                      toxicokinetics, and identify metabolites.
                      Bioavailabillty, elimination, dose-
                      related changes in metabolic pathways,
                      individual variability, time course of
                      effects, interactions between chemicals,
                      and interactions between chemical and
                      environmental/biobehavioral processes
                      (stressors, workload/respiratory Tate)'are
                      factors that are generally easier to ^' -••"•
                      collect under controlled conditions.••'•  •
                        Other goals of laboratory studies
                      include the indepth characterization of
                      effects, the development of new
                      assessment methods, and tha
                      examination of the sensitivity,
                      specificity, and reliability of
                      neurobehavioral assessment methods
                      across chemical classes. The laboratory
                      is die most appropriate setting for the
                      study of environmental and
                      biobehavioral variables that affect the *
                      action of chemical agents. The effects of
                      ambient temperature, task difficulty.
                      rate of ongoing behavior, conditioning
                      variables, tolerancs/sensitiziition, sleep
                      deprivation, motivation, and so forth are
                      sometimes studied.
                        From a.methodologic standpoint,  '
                      human laboratory studies can be
                      divided'into two categories—between-
                      subjects-and within-subjects designs. In
                      the former, the neurobehavioral
                      performance of exposed volunteers is
                      compared with that of nonexposed .
                      participants. In the latter, preexposure
                      performance is compared with -
                      neurobehavioral function under the
                      influence of the chemical or drug.
                      Within-subjects designs havo the
                      advantage of requiring fewer
                      participants, eliminating individual
                      differences as a source of variability.
                      and controlling for chronic mediating
                      variables, such as caffeine use and
                      educational achievement. A
                      disadvantage of the within-subfects
                      design is that neurobehavioral tests
                      must be administered more than once.
                      Practice on many neurobehavioral tests
                      often leads to unproved  performance
                      that may confound the effect of the
                      chemical/drug; There should be a
                      sufficient number of test sessions in the
                      pre-exposure phase of the study to allow
                      performance on all tests to achieve a
                      relatively stable baseline level.
                       'Participants in laboratory exposure
                      studies may have been recruited from
 populations of persons^afready exposed
 to the chemical)drug or from naive "
 populations. Although the use of
 exposed volunteers has ethical
 advantages, can mitigate against  novelty
 effects", and allows evaluation of
 tolerance/sensitization. finding an
 accessible exposed population in-
 reasonable proximity to the laboratory is
 difficult. Naive participants are more
 easily recruited but may differ
 significantly in important characteristics
 from a representative sample of exposed
 persons. Naive volunteers are often
 younger, healthier, and better educated
 than the populations exposed
 environmentally, in the workplace, or
 pharmacotherapeuticaUy.  "'    s
 ' Compared with workplace arid//:
 environmental exposures, laboratory
 exposure conditions can be controlled
 more precisely, but exposure periods are
 much shorter. Generally only one or two
 relatively pure chemicals'are studied for
 several hours while the population of
 interest may be exposed to multiple
 chemicals containing impurities  for
 months or years. Laboratory studies are
 therefore better at identifying and
 characterizing effects with acute  onset
 and the selective effects of pure agents.
  Neurobehavioral test methods  may
 have been selected according to several-
 strategies. A test battery that examines
 multiple neurobehavioral functions may
 be more useful for screening and the
 initial characterization of acute effects.
 Selected neurobehavioral tests that   •
 measure a more limited number of
 functions in multiple ways may be more
 useful for elucidating mechanisms or
 validating specific effects.
  Both chemical and behavioral control
 procedures are valuable for examining
 the specificity of the effects. A
 concordant effect among different
 measures of the same neurobehavioral
 function (e.g., reaction time) and  a lack
 of effect on some other measures  of
 psychomotor function (e.g., untuned
 manual dexterity) would increase the
confidence in a selective effect on motor
 speed and not on attention or
 nonspecific motor function. Likewise.
 finding concordant effects among
 similar chemical or drug classes along
with different effects from dissimilar
classes would support the specificity of
chemical effect. For example, finding
that the effects of a solvent were similar
to those of ethanol but not caffeine
would support the specificity of solvent
effects on a given measure of
neurotoxicity.

2. Animal Studies
  This section provides an overview of
the major types of end points that may
be evaluated in animal neurotoxicity

-------
 52040
Federal  Register ,  Vol.  so.  No.  192 / Wednesdav.  Oc:ober 4.  1995
 studies, describes :r.e Kinds of effects
 that may be ooserved and some of the
 tests used to detect and quantify these
 effects, and provides guidance for
 interpreting data. Compared with
 human studies, animal studies are more
 often available for specific chemicals,
 provide more precise exposure
 information, and control environmental
 factors better (Anger. 1984). For these
 reasons, risk assessments tend to rely
 heavily on animal studies.
   Many tests that can measure some
 aspect of neurotoxicity have been used
 in the field of neurobiology in the last
 50 years. The Office of Prevention.
 Pesticides and Toxic Substances
 (OPPTS) has published animal testing
 guidelines that were developed in
 cooperation with the Office of Research
 and Development (U.S. EPA. 1991a).
 While the test end points included serve
 as a convenient focus for this section,
 there are many other end points for
 which there are no current EPA
 guidelines. The goal of this document is
 to provide a framework for interpreting
 data collected with tests frequently used
 by neurotoxicplogists.
   Five categories of end points will be
 described: Structural or
 neuropathological, neurophysiological,
 neurochemical. behavioral, and
 developmental end points. Table 1 lists
 a number of end points in each of these
 categories.
 Table 1.—Example* of Possible Indicators of
 a Neurotoxic Effect.
 I. Structural or Neuropathological End Points
   1. Gross changes in morphology, including
    brain'weight
   2. Hemorrhage in nerve tissue
  3. Breakdown of neurons, giial cells
  4. Accumulation, proliferation, or
    rearrangement of structural elements
  5. dial fibriliary acidic protein increases
    (in adults]
 II. Neurochamieal End Points
  1. Alterations in synthesis, release, uptake,
    degradation of neurotransmitters
                        2. Alterations in second messenger
                          associated signal transduction
                        3.'Alterations in membrane-bound
                          enzymes regulating neuronal activity
                        4. Inhibition of neuropathy target enzyme
                      in. Neurophysiological End Points
                        1. Change in velocity, amplitude, or
                          refractory period of nerve conduction
                        2. Change in latency or amplitude of
                          sensory-evoked potential
                        3. Change in electroeucephalographic
                          pattern
                      IV. Behavioral and Neurological End Points
                        1. Increases or decreases in motor activity
                        2. Changes in touch, sight, sound, taste, or
                          smell sensations
                        3. Changes in motor coordination.
                          weakness, paralysis, abnormal
                          movement or posture, tremor, ongoing
                          performance
                        4. Absence or decreased occurrence.
                          magnitude, or latency of sensorimotor
                          reflex  '
                        5. Altered magnitude of neurological
                          measurement, including grip strength,
                          hindlimb splay
                        6. Seizures
                        7. Changes in rate or temporal patterning
                          of schedule-controlled behavior
                        8. Changes in laming, memory,
                          intelligence, attention
                      V. Developmental End Points
                        1. Chemically induced changes in the time
                          of appearance of behaviors during
                          development
                        2. Chemically induced changes in the
                         growth or organization of structural or
                          neurochemical elements.
                        a. Structural End Points of
                      Neurotoxicity. Structural end points are
                      typically denned as neuropathological
                      changes measured through gross
                      observation or with the aid of a
                      microscope. Gross changes in
                      morphology can include discrete or
                      widespread lesions in nerve tissue.
                      Changes in brain size (weight, width, or
                      length) are considered to be indicative
                      of neurotoxic events. This is true
                      regardless of changes in body weight.
                      because brain size is generally protected
                      during undemutrition or .weight loss.
 unlike many other organs or tissues. It
 is inappropriate to express brain weight
 changes as a ratio of body weight and
 thereby dismiss changes in absolute
 brain weight. The risk assessor should
 be aware that a unit of measurement
 that is biologically meaningful should
 be used for analysis. Brain length
' measurements, for example, expressed
 to 1 or 10 micron units is biologically
 meaningless. The same is true for brain
 width.
   Neurons are composed of aneuronal
 body, axon,  and dendritic processes.
 Various types of neuropathological
 lesions may  be classified according to,
 the site where they occur (WHO, 198a;
 Krinke, 1989: Griffin, 1990).        H
-Neurodegenerative lesions in the central
 or peripheral nervous system may be
 classified as a neuronopathy (changes in
 the neuronal cell body), axonopathy
 (changes  in the axons), myelinopathy
 (changes  in the myelin sheaths), or
 terminal degeneration. For
 axonopathies, a more precise location of
 the changes  may also be described (i.e.,
' proximal, central, or distal axonopathy).
 In the case of some developmental
 exposures, a neurotoxic chemical might
 delay or accelerate the differentiation or
 proliferation of cells or cell types.
 Alteration in the axonal termination site
 might also occur with exposure. In an
 aged population, exposure to some
 neurotoxicants might accelerate the
 normal loss of neurons associated with
 aging (Reuhl, 1991). In rare cases,
 neurotoxic agents have been reported to
 produce neuropathic conditions
resembling neurodegenerative disorders
 in humans such as Parkinson's disease
 (WHO, 1986). Table 2 lists examples of
such neurotoxic chemicals, their
putative site  of action, the type of
neuropathology produced, and the
disease or condition that each typifies.
                    TABLE 2.—NEUROTOXICANTS AND DISEASES WITH SPECIFIC NEURONAL TARGETS
Site of action
Neuron cell body •• 	 .
Nerve terminal 	
Schwann cell Myelin —
Centra>penpheral distal
axon.
Central axons 	 	
Proximal axon . 	 . 	

Neuropathology
Neuronopathy 	
Terminal destruction .„.
MyeKnopathy 	 . 	
Distal axonopathy 	
Central axonopattiy ..
Proximal axonopathy ...

Neurotoxicant
.Metfiyhnercury Qunofnic acid 3-
Acetylpyridine.
1-MethyM-pnenyi-1 ,2,3,6-
tetrahydropyriolne (oopamtoergic).
HexacNorophene 	
Acrylamide Carbon dsulfide n-Hexane .....
Clioqutnol
B.BMrninodiproptonitrihi .

Corresponding neurodegenerative disease or
condition
Minamata disease, Huntington's disease, Cere-
bellar ataxia.
Parkinson's Disease.
Congenital hypomyelinogenesis.
Peripheral neuropathy.
Suoacute rnyeJoopticoneuropathy
Motor neuron disease •

  Alterations in the structure of the
nervous system (i.e., neuronopathy,
axonopathy, myelinopathy, terminal
                     degeneration) are regarded as evidence
                     of a neurotoxic effect. The risk assessor
                     should note that pathological changes in
many cases require time for the
perturbation to become observable,
especially with evaluation at the light

-------
Federal
Register
•' Vol.
60.
Mo.
192
/ Wednesday,
October
•i^^^^^^
4.
1995
/ N'otices
52041
  microscopic level. N'europathological
  studies should control for potential
  differences in the area(s) and section(s)
  of the nervous system sampled, in the
  age, sex, and body weight of the subject,
  and in fixation artifacts (WHO, 1986).
  Concern for the structural integrity of
  nervous system tissues derives from its
  functional specialization and the lack of
  regenerative capacity in the central
  nervous system.
   In general, chemical effects can lead
  to two types of structural alteration at
  the cellular level: the breakdown of
  cells, in whole or in part, or the
  accumulation, proliferation, or
  rearrangement of structural elements  •
  (e.g., intermediate filaments,
  microtubules) or organelles (e.g.,
  mitochondria). Some changes may be
 associated with regenerative processes
 that reflect adaptive changes associated
 with exposure to a toxicant.
   Chemically induced injury to the
 central nervous system may be
 associated with astrocytic hypertrophy.
 Such changes may be seen using
 immunocytochemical techniques
 visualized by light microscopy or
 quantified more precisely by
 radioimmunoassay (RIA) procedures.
 Assays of glial fibrillary acidic protein
 (GFAP), the major intermediate filament
 protein of astrocytes, have been
 proposed as a biomarker of this
 response (O'Callaghan. 1988). The
 interpretation of a-chemical-induced
 change in GFAP is facilitated by
 corroborative data from the
 neuropathology or neuroanatomy
  evaluation.*A number of chemicals
  known to injure;.the central nervous
  system, including trimethyltin,
  methylmercury, cadmium, 3-
  acetylpyridine, and
  methyl pheny Itetrahy dro pyridine-
  (MPTP), have been shown to increase
  levels of GFAP. Measures of GFAP are
  now included in the Neurotoxicity Test
  Battery testing guidelines (U.S. EPA,
  1991a).
   Increases in GFAP above control
 .levels may be seen at dosages below
  those necessary to produce damage seen
  by standard microscopic or
  histopathological techniques. Because
  increases in GFAP reflect an astrocyte
  response in adults, treatment-related
  increases in GFAP are considered to be
  evidence that a neurotoxic effect has
  occurred. Decreases in GFAP are not
  clearly interpretable as indicative of
  neurotoxicity. The absence of a change
  in GFAP following exposure does not
  necessarily mean that the chemical is
  devoid of neurotoxic potential Known
  neurotoxicants such as cholinesterase-
  inhibiting pesticides, for example.
 would not be  expected to increase brain
 levels of GFAP. Interpretation of GFAP
 changes prior to weaning is confounded
 by the possibility that chemically
 induced increases in GFAP may be
 masked by changes in the concentration
 of this protein associated with
 maturation of the central nervous
 system, and these data may be difficult
 to interpret
   b. Neurophysiological End Points of
 Neurotoxicity. Neurophysiological
  studies are those that measure the
  electrical activity of the nervous svstem.
  The term "neurophysiology" is often
  used synonymously with,
  "electrophysiology" (Dyer, 1987).
  Neurophysiological techniques provide
  information on the integrity of defined
  portions of the nervous system. Several
 . neurophysiological procedures are
  available for application to
  neurotoxicological studies. Examples of
  neurophysiological measures, of
  neuro.toxicity are listed in Table 3. They
  range in scale from procedures that
  employ microelectrodes to study the
  function of single nerve cells or
  restricted portions of them, to       /
  procedures that employ macroelectrbdes
  to perform simultaneous recordings of
  the summed activity of many cells.
  Microelectrode procedures typically are
  used to study mechanisms of action and
  are frequently performed in vitro.
  Macroelectrode procedures are generally
  used in studies to detect or characterize
  the potential neurotoxic effects of agents
  of interest because of potential
 environmental exposure. The present
 discussion concentrates on
 macroeiectrode neurophysiological
 procedures because it is more likely that
 they will be the focus of decisions
 regarding critical effects in risk
 assessment All of the procedures
 described below for use in animals also
 have been used in humans to determine
 chemically induced alterations in
 neurophysiological function.
                    TABLE 3.—EXAMPLES OF NEUROPHYSIOLOGICAL MEASURES OF NEUROTOXICTTY
Systenvfunction
Retina 	 : 	 _
Visual pathway 	 	
Visual function 	 	
Audtory pathway 	 _ 	
Audrtory function 	 	 	 	
Somatosensory pathway
Somatosensory function ... 	 	 	
Spinocerebellar pathway 	 	 	
Mixed nerve 	 	 ..._. 	 	
Motor axons 	 	 	 ; 	 .„ „.'
Sensory axons 	 	 	
Neuromuscular 	 „„_
General central nervous system/level of arous-
al. • .
Procedure
Etectroretinograpny (ERG) ._ 	
Flash evoked potential (FEP)

and contrast).
Brain «tftnt aitfftrw ounfcA/4 rwt***i4iAi /QACO*
(Cfcta).
BAER (tones)

Somatosentory... evokacv potential (SEP)
(shocks).
SEP (tactile) „
SEP recorded from cerebellum 	
(PNAP).
PNAP isolate motor components
PNAP isolate sensory components 	
Etectromyograpriy (EMG). H-reftex, M-re-
spons*.
Electroenceprialography (EEG) 	

Representative agents
Oevetoprrwntal leadi.
Carbon dsurrkto. • • •
Carbon <£sur5de.
AnwogrycosuJe, Antibiotics, Toluene, styrene.
Ammogrycoside, Antibiotics, Toluene, styrene.
Aerytamide, rvHexane.
Afifvianwte rvHAvji/^
Acrytamide rhHexarw.
Trwtnyltin.
Triethyltin.
Otthiobiuret
Anesthetics.

  (1) Nerve conduction studies. Nerve
conduction studies, generally performed
on peripheral nerves, can be useful in
investigations of possible peripheral
neuropathy. Most peripheral nerves
contain mixtures of individual sensory
and ihotor nerve fibers, which may or
may not be differentially sensitive to
neurotoxicants. It is possible to
distinguish sensory from, motor effects
in peripheral nerve studies by
measuring activity in purely sensory

-------
 52042
Federal  Register    Vol. 60,  N'o. 192  /  Wednesday.  October  4. 1995  /  Notices
r.erves such as the su.-ai nerve or by
measuring the muscle response evoked
by nerve stimulation to measure motor
et'fects. While a number of end points
can be recorded, the most critical
variables are (1) nerve conduction
velocity. (2) response amplitude, and (3)
refractory period.
  .Verve conduction measurements are
influenced by a number of factors, the
most important of which is temperature.
An adequate nerve conduction study
will either measure the temperature of
the limb under study and
mathematically adjust the results
according to well-established
temperature factors or control limb
temperature within narrow limits.
Studies that measure peripheral nerve
function without regard for temperature
are not adequate for risk assessment.
  In well-controlled studies, statistically
significant decreases in nerve
conduction velocity are indicative of a
neurotoxic effect. While a decrease in
nerve conduction velocity is indicative
of demyelination. it frequently occurs
later in the course of axonal degradation
because normal conduction  velocity
may be maintained for some time in the
face of axonal degeneration. For this
reason, a measurement of normal nerve
conduction velocity does not rule out
peripheral axonal degeneration if other
signs of peripheral nerve dysfunction
are present.
  Decreases in response amplitude
reflect a loss of active nerve  fibers and
may occur prior to decreases in
conduction velocity in the course of
peripheral neuropathy. Hence, changes
in response amplitude may be more
sensitive measurements of axonal
degeneration than conduction velocity.
Measurements of response amplitude,
however, can be more variable and
require careful application of
experimental techniques, a larger
sample size, and greater statistical
power than measurements of velocity to
detect changes. The refractory period
refers to the time required after
stimulation before a nerve can fire again
and provides a measure reflecting the
functional status of nerve membrane ion
channels. Chemically induced changes
in refractory periods in a well-
controlled study indicate a neurotoxic
effect.
  In summary, alterations in peripheral
nerve response amplitude and refractory
period in studies that are well
controlled for temperature are indicative
of a neurotoxic effect. Alterations in
peripheral nerve function are frequently
associated with clinical signs such as
numbness, tingling, or burning
sensations or with motor impairments
such as weakness. Examples of
                      compounds that alter peripheral nerve
                      function Ln humans or experimental
                      animals include acrylamide, carbon
                      disulfide. n-hexane, lead, and some
                      organophosphates.
                        (2) Sensory, motor, and other evoked
                      potentials. Evoked potential studies are
                      electrophysiologicai procedures that
                      measure the response elicited from a
                      defined stimulus such as a tone; a light,
                      or a brief electrical pulse. Evoked
                      potentials reflect the function of the
                      system under study, including visual.
                      auditory, or somatosensory; motor
                      involving motor nerves and innervated
                      muscles; or other neural pathways in
                      the central or peripheral nervous system
                      (Rebert, 1983; Dyer, 1985; Mattsson and
                      Albee, 1986: Mattsson et al., 1992;
                      Boyes, 1992,1993). Evoked potential
                      studies should be interpreted with
                      respect to the known or presumed
                      neural generators of the responses, and
                      their likely relationships with
                      behavioral outcomes, when such
                      information is available. Such
                      correlative information strengthens the
                      confidence in electrophysiologicai
                      outcomes. In the absenca of such
                      supportive information, the extent to
                      which evoked potential studies provide
                      convincing evidence of neurotoxicity is
                      a matter of professional judgment on a
                      case-by-case basis.  Judgments should
                      consider the nature, magnitude, and
                      duration of such effects, along with
                      other factors discussed elsewhere in this
                      document
                        Data are in the form of a voltage
                      record collected over time and can be
                      quantified in several ways. Commonly,
                      the latency (time from stimulus onset)
                      and amplitude (voltage) of the positive
                      and negative voltage peaks are
                      identified and measured. Alternative
                      measurement schemes may involve
                      substitution of spectral phase or
                      template shifts for peak latency and
                      spectral power, spectral amplitude, root-
                      mean-square, or integrated area under
                      the curve for peak amplitude. Latency
                      measurements are dependent on both
                      the velocity of nerve conduction and the
                      time of synaptic transmission. Both of
                      these factors depend on temperature, as
                      discussed in regard to nerve conduction,
                      and similar caveats apply for sensory
                      evoked potential studies. In studies that
                      are well controlled for temperature.
                      increases in latencies or related
                      measures can reflect deficits in nerve
                      conduction, including demyelination or
                      delayed synaptic transmission, and are
                      indicators of a neurotoxic effect.
                       Decreases in peak latencies, like
                      increases in nerve conduction velocity.
                      are unusual, but the neural systems
                      under study in sensory evoked
                      potentials are complex, and situations
  that might cause a peak measurement to
  occur earlier are conceivable. Two sueh
  situations are a reduced threshold for
  spatial or temporal summation of
  afferent neural transmission and a
  selective loss of cells responding late in
  the peak, thus making the measured
  peak occur earlier. Decreases in peak
  latency should not be dismissed
  outright as experimental or statistical
  error, but should be examined carefully
  and perhaps replicated to assess
,  possible neurotoxicity. A decrease in
  latency is not conclusive evidence of a
  neurotoxic effect
    Changes in peak amplitudes or
  equivalent measures reflect changes in  t
  the magnitude of the neural population tj
  responsive to stimulation. Both       >]
  increases and decreases in amplitude
  are possible following exposure to.
  chemicals. Whether excitatory or
  inhibitory neural activity is translated
  into a positive or negative deflection in
  the sensory evoked potential is
  dependent on the physical orientation
  of the electrode with respect to the
  tissue generating the response, which is
  frequently unknown. Comparisons
  should be based on the absolute change
  in amplitude. Therefore, either increases .
  or decreases in amplitude may be
  indicative of a neurotoxic effect.
    Within any given sensory system, the
  neural circuits that generate various
  evoked potential peaks differ as a
  function of peak latency. In general,
  early latency peaks reflect the
  transmission-of afferent sensory
  information. Changes in either the
  latency or amplitude of these peaks are
  considered convincing evidence of a
  neurotoxic effect that is likely to be
  reflected in deficits in sensory
  perception. The later-latency peaks, in
  general, reflect not only the sensory
  input but also the more nonspecific
  factors such as the behavioral state of
  the subject, including such factors as
  arousal level, habituation, or
  sensitization (Dyer, 1987). Thus,
  changes in later-latency evoked
  potential peaks must be interpreted in
  light of the behavioral status of the
  subject and would generally be
  considered evidence of a neurotoxic
  effect.
   (3) Seizures/convulsions.
  Neurophy siological recordings of brain
  electrical activity that demonstrate
  seizure-like activity are indicative of a
  neurotoxic effect Occasionally,
  behaviors resembling convulsions might
  follow actions outside the nervous
  system, such as direct effects on muscle.
  When convulsion-like behaviors are
  observed, as described in the behavioral
  section, neurophysiological recordings
  can determine if these behaviors

-------
                 Federal  Register / Vol. 60. No. 192  / ..Wednesday, October 4.  1995 ' Notices
                                                                     52043
originate from seizure activity in the
brain.
  In addition to producing seizures
directly, neurotoxicants also may alter
the frequency, severity, duration, or
threshold for eliciting seizures produced
through other means. Such changes can
occur after acute exposure or after
repeated exposure to dose levels below
the acute threshold and are considered
to be neurotoxic effects. Examples of
agents that produce convulsions include
lindane, DDT (dichloro-diphenyl-
trichloroethane), pyrethroids, and
trimethyltin.
  (4) Electroencephalography (EEC).
EEC analysis is used widely in clinical
settings for the diagnosis of neurological
disorders and less often for the
detection of subtle toxicant-induced
dysfunction (WHO, 1986; Eccles. 1988).
The basis for using EEG in either setting
is the relationship between specific
patterns of EEG waveforms and  specific
behavioral states. Because states of
alertness and stages of sleep are
associated with distinct patterns of
electrical activity in the brain, jt.is.
generally thought" that arousal; level can
be evaluated by monitoring the EEG.
  Dissociation of EEG activity and
behavior can. however, occur after
exposure to certain chemicals. Normal
patterns of transition between sleep
stages or between sleeping and waking _
states are known to remain disturbed for
prolonged periods of time after exposure-
to some chemicals. Changes in the
pattern of the EEG can be elicited by
stimuli producing arousal (e.g., lights,
sounds) and anesthetic drugs. In studies
with toxicants, changes in EEG pattern
can sometimes precede alterations in
other objective signs of neurotoxicity
(Dyer, 1987).
  EEG studies must be done under
highly controlled conditions, and the
data must be considered on a case-by-
case basis. Chemically induced seizure
activity detected in the EEG pattern is
evidence of a neurotoxic effect,
  c. Neurochemical End Points of
Neurotoxicity, Many different
aeurochemical end points have been
measured in neurotoxicological studies,
and some have proven useful in
advancing the understanding of
mechanisms of action of neurotoxic
chemicals (Bondy, 1986; Mailman,
1987; Morell and Mailman, 1987; Costa,
1988). Normal functioning of the
nervous system depends on the
synthesis and release of specific
neurotransmitters and activation of their
receptors at specific presynaptic and
postsynaptic sites. Chemicals can
interfere with the ionic balance of a,
neuron, act as a cytotoxicant after
transport into a nerve terminal, block
reuptake of neurotransmitters and their
precursors,  act as a metabolic poison J
overstimulate receptors, block      /
transmitter release, and inhibit
transmitter synthetic or catabolic
enzymes. Table 4 lists several chemicals
that produce neurotoxic effects at the
neurochemical level (Bondy,  1986;
Mailman. 1987; Morell and Mailman,
1987; Costa, 1988).
                TABLE 4.—EXAMPLES OF NEUROTOXICANTS Wrm KNOWN NEUROCHEMICAL MECHANISMS
                       Site of action
                                            Example*
 1. Neurotoxicants Acting on Ionic Balance:
    A. Inhibit sodium entry  	
    B. Block dosing of sodhjm channel ....
    C. Increase permeability to sodium ....
    0. Increase intracelluiar calcium		
 2. Cytotoxicanta—Depend on uptake into nerve terminal.
 3. Uptake blockers .._.__.	„..._.._„_
 4. Metabolic poisons  		„„	._.._..	
 5. Hyperactrvation of receptors 		
 6. Blocks transmitter release (AcetytehoKne [AChJ) ,
 7. Inhibition of transmitter degradation (ACn)
 8. Blocks axonai transport			
                   TeliodotoxirL
                   pjj'-OOT, pyrettiroids.
                   Bafrachotaort
                   Chtofdecone.
                   MPTP.
                   Henvcfaofiniunx
                   Cyanide..
                   Demote acid.
                   BoftJnun toxin.
                   Pesticides of the organopnosphate and carbamate ctasse*.
                   Acrytamide.
  As stated previously, any
neurochemical change is potentially
neurotoxic. but each determination
requires professional judgment.
Persistent or irreversible chemically
induced neurochemical changes are
indicative of neurotoxicity. Because the
ultimate functional significance of some
biochemical changes is not known at
this time, neurochemical studies should
be interpreted with reference to the
presumed neurotoxic consequence(s) of
the neurochemical changes. For
example, many neuroactive agents can
increase or decrease neurotransmitter
levels, but such changes are not
necessarily indicative of a neurotoxic
effect. If, however, these neurochemical
changes may be expected to have
neurophysiological, neuropathological.
or neurobehavioral correlates, then the
neurochemical changes could be
classified as neurotoxic effects.
  Some neurotoxicants, such as the
orgmnophosphate and carbamate
pesticides, are known to inhibit the
activity of a specific enzyme,
acetylcholinesterase (for a review sea
Costa. 1988), which hydrolyzest the
neurorransmitter acetylcholine.
Inhibition of the enzyme prolongs the
action of the acetylcholine at the
neuron's synaptic receptors and is
responsible for the autonomic
stimulation and death that them agents
cause.
  Within EPA and elsewhere, questions
have arisen as to whether inhibition of
cholinestense activity constitutes an
adverse effect for defining hazard
potential and evaluating risk. There is
agreement among scientists that
statistically significant inhibition of
cholinesterase activity in multiple
organs and tissues accompanied by
clinical effects constitutes a hazard.
However, there is scientific uncertainty
and related controversy aboutthe risk
assessment implications of data
describing inhibition of cholinesterase
enzyme activity in the absence of
observable clinical effects. While there
is agreement that such inhibition is a
biomarker of exposure, there is
continued disagreement over whether  •
cholinesterase inhibition^especially in
blood, constitutes an adverse effect.
  At this point, it can be stated that
there is general agreement among
scientists that objective clinical
measures of dysfunction/impairment
can be overt manifestations of inhibition
of cholinesterase in the nervous system.
On the basis of Hiniml manifestations.
e.g.. muscle weakness, tremor, blurred
vision, one should be able to evaluate
dose-response and dose-effect
relationships and define the presence
and absence of given effects. A
relationship between the effect and
cholinesterase inhibition should be

-------
 52044
Federal  Register / Vol. 60. No.- 192 / Wednesday. October 4.  1995 / .Notices
 confirmed by biochemical measures of
 reduced cholinesterase activity.
   In addition, a reduction in brain
 cholinesterase activity may or may not
 be accompanied by clinical
 manifestations. Most experts in the field
 acknowledge that when significant
 reductions in brain cholinesterase
 activity alone occur, reduced
 cholinesterase levels either are
 themselves toxic or would lead to a
 neurotoxic effect if exposure were to
 persist over time or increase in
 magnitude. Therefore, statistically
 significant decreases in brain
 cholinesterase could be considered to be
 a biologically significant effect.  •
   A reduction in RBG and/or plasma
 cholinesterase activity also may or may
 not be accompanied by clinical
 manifestations. At this time, there is
 general agreement that the observation
 of inhibition of RBC and/or plasma
 cholinesterasa contributes to the overall
 hazard identification of cholinesterasa
                      inhibiting agents by serving as
                      biomarkers. As such, these enzyme
                      parameters can provide information that
                      will help scientists evaluate whether
                      reported clinical effects are associated
                      with cholinesterase inhibition. There
                      remains, however, a lack of consensus
                      as to whether RBC and/or plasma
                      cholinesterase represent biologically
                      significant events. Discussions on this
                      topic are continuing within the Agency.
                       A subset of organophosphate agents
                      also produces organophosphate-induced
                      delayed neuropathy (OPIDN) after acute
                      or repeated exposure. Prolonged
                      inhibition (i.e.. aging) of neurotoxic
                      esterase (or neuropathy target enzyme)
                      has been associated with agents that
                      produce OPIDN (Johnson, 1990), a clear
                      neurotoxic effect
                       d. Behavioral'End Points of
                      Neurotoxicity. EPA's testing guidelines
                      developed for the Toxic Substances
                      Control Act and the Federal Insecticide,
                      Fungicide and Rodentitide Act describe
 the use of functional observational
 batteries (FOB), motor activity, and
 schedule-controlled behavior for
 assessing neurotoxic potential (U.S.
 EPA, 1991a). There are many other
 measures of behavior, including
 specialized tests of motor and sensory
 function and of learning and memory
 (Tilson. 1987; Anger. 1984). Examples of
 behavioral end points that have been
 used to detect neurotoxicity are
 included in Table 1. The risk assessor
 should know that the literature is'clear
 that a number of other behaviors besides
 those listed in Tables 1 and 5 could be
 affected fay chemical exposure. For
 example, alterations in food and water   ^
 intake, reproduction, sleep, temperature'
 regulation, and circadian rhythmicity  *
 are controlled by specific regions of the
 brain and chemical-induced alterations
 in these behaviors could be indicative of
 neurotoxicity. It is reasonable to assume
 that a NOAEL or LOAEL could be based
 on one or more of these end points.
   TABLE 5.—SUMMARY OF MEASURES IN A REPRESENTATIVE FUNCTIONAL OBSERVATIONAL BATTERY, AND THE TYPE OF
                                             DATA PRODUCED BY EACH
Home cage and open field
Posture (D)
Convulsions, tremors (D)
Palpetxal closure (R)
LacrtmaHon (R)
PiloerectJon (Q)
Salivation (R)
Vocalizations (Q)
Rearing (C)
Urination (Q
Defecation (C)
Gait (D, R)
Arous* (R)
Mobility (R).
Sterectypy (D).
Biza/re behavior (D)
Manipulative
Ease of removal (R)
HandBng reactivity (R)
Palpetoral closure (R).
Approach response (R).
CBck response (R).
Touch response (R).
Tail pinch response (R).
Higjrang renex (n).
Landing foot splay (1).
ForeKmb grip strength (1).
HindUmb grip strength (1).
Pupil response- (Q).
Physiologic
Body temperature (1).
Body weight (1).
£>
  D—-descriptive data; R—rank order data; Q—quanta! data; I—interval data; C—court data.
  Behavior is an indication of the
overall well-being of the organism.
Changes in behavior can arise from a
direct effect of a toxicant on the nervous
system or indirectly from its effects on
other physiological systems.
Understanding the interrelationship
between systemic toxicity and
behavioral changes is extremely
important (e.g.. the relationship between
Uver damage and motor activity). The
presence of systemic toxicity may
complicate, but does-not necessarily
preclude, interpretation of behavioral
changes as evidence of neurotoxicity. In
addition, a number of behaviors (e.g..
schedule-controlled behavior) may
require a motivational component for
successful completion of the task. In  '
such cases, experimental paradigms
designed to assess the motivation of an
                     animal during behavior might be
                     necessary to interpret tha meaning of
                     some chemical-induced changes in
                     behavior.
                       The following sections describe in
                     general behavioral tests and their uses
                     and offer guidance on interpreting data.
                       (1) Functional observational battery.
                     A functional observational battery is
                     designed to detect and quantify major
                     overt behavioral, physiological, and
                     neurological signs (Gad. 1982;
                     OTJonoghue, 1989; Moser, 1989). A
                     number of batteries have been
                     developed, each consisting of tests
                     generally intended to evaluate various
                     aspects of sensorimotor function (Tilson
                     and Moser. 1992). Many FOB tests are
                     essentially clinical neurological
                     examinations that rate the presence or
                     absence, and in many cases the severity,
of specific neurological signs. Some
FOBs in animals are similar to clinical
neurological examinations used with
human patients. Most FOBs have
several components or tests. A typical
FOB is summarized in Table 5 and
evaluates several functional domains,
including neuromuscular (i.e.,
weakness, incoordination. gait, and
tremor), sensory (i.e., audition, vision.
and somatosensory), and autonomic
(i.e., pupil response and salivation)
function. FOB data may be in the form
of interval, ordinal, or continuous
measurements.
  The relevance of statistically
significant test results from  an FOB is
judged according to the number of signs
affected, the dose(s) at which effects ar»
observed, and the nature, severity, and
persistence of the effects and their

-------
                 Federal  Register / Vol. 60. No.  192 /• Wednesday. October 4. 1995.;  N'otices
                                                                    52045
incidence in relation to control animals.
If only a few unrelated measures in the
FOB are affected, or the effects are
unrelated to dose, the results are not
considered evidence of a neurotoxic
effect. If several neurological signs are •
affected but only at the high dose and
in conjunction with other overt signs of
toxicity, including systemic toxicity,
large decreases in body weight,
decreases in body temperature, or
debilitation, there is ncr conclusive
evidence of a direct neurotoxic effect. In
cases where several related measures in
a battery of tests are affected and the
effects appear to bo dose dependent, the
data are considered to be evidence of a
neurotoxic effect, especially in the
absence of systemic toxicity. Recently, it.
was proposed that data from FOB
studies be grouped into several .
neurobiological domains, including
neuromuscular (i.e., weakness,
^coordination, abnormal movements,
gait), sensory (i.e. auditory, visual,. '
somatosensory), and autonomic
functions (Tilson andMoser. 1992).
This statistical technique is useful when
separating changes that occur on the
basis of chance or in conjunction with
systemic toxicity from those treatment-
related changes indicative of neurotoxic
effects. In the case of the developing
organism, chemicals may alter the
maturation or appearance of
sensorimotor reflexes. Significant
alterations in or delay of such reflexes
is evidence of a neurotoxic effect.
  Examples of chemicals that affect
neuromuscular function are 3-
acetylpyridine, acrylamide, and
triethyltin. Organophosphate and
carbamate insecticides produce
autonomic dysfunction, while
organochlorine and pyrethroid
insecticides increase sensorimotor
sensitivity, produce tremors, and in
some cases, cause seizures and
convulsions (Spencer and Schaumberg.
1980).
  (2) Motor activity. Motor activity
represents a broad class of behaviors
involving coordinated participation of
sensory, motor, and integntive
processes. Assessment of motor activity
is noninvasive and has been used to
evaluate the effects, of acute and
repeated exposure to neurotoxicants
(MaePhail et aL, 1989). An organism's
level of activity can, however, be
affected by many different types of
environmental agents-, including
nonneurotoxic agents. Motor activity
measurements also have been used in
humans to evaluate disease states.
including disorders of the nervous
system (Goldstein and Stein, 1985).
  Motor activity is usually quantified as
the frequency of movements over a
period of time. The'-total counts
generated during a test period will
depend on the recording mechanism
and size and configuration of the testing
apparatus. Effects of agents on motor
activity can be expressed as absolute
activity counts or as a percentage of
control values. In some cases, a
transformation (e.g.. square root) may be
used to achieve a normal distribution of
the data. The frequency of-motor
activity within a session usually
decreases and is reported as the average
number of counts occurring in each
successive block of time. The EPA's
Office of Prevention, Pesticides and
Toxic Substances guidelines (U.S. EPA,
1991a), for example, call for test-
sessions of sufficient duration to allow
motor activity to approach steady-state
levels during the last 20 percent of the
session for control animals. A sum of
the counts in each epoch will add up to
the total number of counts per session.
  In the adult, nourotoxic agents
generally decrease motor activity
(MaePhail et aL, 1989). Examples
include many pesticides (e.g.,
carfaamates. chlorinated hydrocarbons,
organophosphates, and pyrethroids).
heavy metals (lead, tin, and mercury),
and other agents (3*acatylpyridine,-
acrylamide, and 2,4-dithiobiuret). Some
neurotoxicants (e.g., toluene, xylene.
triadimefon) produce transient increases
in activity by. presumably stimulating
neurotransmitter release, while others
(e.g., trimethyltin) produce persistent .
increases in motor activity by destroying
specific regions of the brain (e.g.,
hippocampus).
  Following developmental exposures,
neurotoxic effects are often observed as
a change in the developmental profile or
maturation of motor activity patterns.
Frequently, developmental exposure to
neurotoxic agents will produce an
increase.in motor activity that persists
into adulthood or that results in changes
in other behaviors. This type of effect is
evidence of a neurotoxic  effect. Like
other organ systems, the nervous system
may be differentially sensitive to
toxicants in groups such as the young.
For example, toxicants introduced to the
developing nervous system may kill
stem cells and thus cause profound •
effects on adult structure and function.
Moreover, toxicants may have greater
access to the developing nervous system
before the blood-brain barrier is
completely formed or before metabolic
detoxifying systems are functional.
  Motor activity measurements are
typically used with other tests (e.g.,
FOB)-to help detect neurotoxic effects.
Agent-induced changes in motor
activity associated with other overt
signs of toxicity (e.g., loss of body
 weight, systemic toxicity) or occurring
 in non-dose-related fashion are of less
 concern than changes that are dose
 dependent, related to structural or other
 functional changes in the nervous
 system, or occur in the absence of life-
 threatening toxicity.
  (3)-Schedule-controlled operant
 behavior. Schedule-controlled operant
 behavior (SCOB) involves the
 maintenance of behavior (e.g.,
 performance of a lever-press or key-peck
 response) by reinforcement. Different
 rates and patterns of responding are
 controlled by the relationship between
 response and subsequent reinforcement.
 SCOB provides a measure of        7
 performance of a learned behavior (e.g.,
 lever press or key peck) and involves
 training and motivational variables that
 must be considered in-'evaluating the
 data. Agents may interact with sensory
 processing, motor output, motivational
 variables (i.e., related to reinforcement),
 training history, and baseline
 characteristics (Bice, 1988: Cory-
 Slechta, 1989). Rates and patterns of
 SCOB display remarkable species and
 experimental generality.
  In laboratory animals. SCOB has been
 used to study a wide range of
 neurotoxicants. including
 methylmercury, many pesticides,
 carbon disulfide, organic and inorganic
 lead, and triethyl and trimethyltin
 (MaePhail. 1985; Tilson, 1987; Rice,
 1988). The primary SCOB end points for
 evaluation are response rate and the
 temporal pattern of responding. These
 end points may vary as a function of the
 contingency between responding and
 reinforcement presentation (i.e.,
 schedule of reinforcement). While most
 chemicals decrease the efficiency of
 responding at some dose, some agents
 may increase, response efficiency on
 schedules requiring  high response rates
 due to a stimulant effect or an increase
 in central nervous system excitability.
 Agent-induced changes in responding.
 between reinforcements (i.e., the
 temporal pattern of responding) may
 occur independently of changes in the
 overall rate of responding. Chemicals
 may also affect the reaction time to
 respond following presentation of a
stimulus. Agent-induced changes in
response rate or temporal patterning
associated with other overt signs of
toxicity (e.g.. body weight loss, systemic
toxicity. or occurring in a non-dose-
related fashion) are of less concern than
changes that are dose dependent, related
to structural or other functional changes
in the nervous system, or occur in the
absence of life-threatening toxicity.
  (4) Convulsions. Observable
convulsions in animals are indicative of
an adverse effect. These events can

-------
52046
Federal  Register / Vol. so.  No. 192  /  Wednesday,  October 4. 1995 / Notices
reflect central nervous system activity
comparable to that of epilepsy in
humans and could be defined as
aeurotoxicity. Occasionally, other toxic
actions of compounds, such as direct
effects on muscle, might mimic some
convulsion-like behaviors. In some
cases, convulsions or convulsion-like
behaviors may be observed in animals
that are otherwise severely
compromised, moribund, OF near death.
                      In such cases, convulsions might reflect
                      an indirect effect of systemic toxicity
                      and are less dearly indicative of
                      neurotoxicity. As discussed in the
                      section on neurophysiological measures,
                      electrical recordings of brain activity
                      could be used to determine specificity
                      of effects on the nervous system.
                        (5) Specialized tests for neurotoxicity.
                      Several procedures have been
                      developed to  measure agent-induced
changes in specific neurobehavioral
functions such as motor, sensory, or
cognitive function (Tilson, 1987; Cory-
Slechta. 1989). Table 6 lists several
well-known behavioral tests, the
neurobehavioral functions they were
designed to assess, and agents known to
affect the response. Many of these tests
in animals have been designed to assess
neural functions in humane using
similar testing procedures.
                TABLE 6.—EXAMPLES OF SPEOAUZED BEHAVIORAL TESTS TO MEASURE NEUROTOXICITY
                Function
                                     Procedure
          Representative agents
    incooFcSnsDsn •
    Tremor —
    Myodooia spasms
Soraory:
    AuoTtory	
    Vouai	.
                       Grip sliefiejlte iwwwnjng dftdurance;
                         sion rod! dacnrrinalive motor function.
                       Rotorod. ga* maasuemana; nghting reflex
                       Rating 3caiet specksl anafystt 	
                       Rating scale, spectral analysis
 n-Hexane. mathJ n-outy*eton«, carbaryt.

 3-Acetylpyriolne, •thanei.
 CHofoacone. Type I pyreflvortt, DOT.
 DDT. Type H |
                                                                                                               /
                       Dtacriminalion coneVoning Reflex modHlcafion
       i. WnethyUta.
    Pain s*ns£vity	
                                   conoMoning (trtration); func-
                                                                              Aaytamide.
                                                                              ParBttion.
      9/Menxxy:
                                          tional otaarvationeJ battery.
                                                    consWoning ._
                                                                              OBseoropyM
    Oa
                xrtng
                                                                  latal meeiyknereuy.
                                                             Ahmnum.
                                                             CaiberyL
                                                             TnineHiyNki, IOPN.
                                                             Neonatal MnettiyMn.
                                                                          ophospnate    (OFP)    Pre/
                                        Delayed matching to sample
                                        RepexHd acQuiafcn	
                                        visual decranras«n	
                                                             PnVheoaatat lead.
                                                             HypetvitHTinois A.
                                                             Styrena.
                                                             DFP.
                                                             TrimostyiBfL
                                                             OFP.
  A statistically significant chemically
induced chang* in any measure in Tab)*
6 is presumptive evidence of advers*
effect Judgments of neurotoxicity may
involve not only tha analysis of change*
seen but the structurs and class of the
chemical and othar available
neurochsmical, neurophysiological, and
neuropathological evidenc*. In general.
behavioral changes seen across broader
dos« ranges indicate mom specific
actions on the systems underlying those
changes, i.e.. the nervous system.
Changes that an not dose dependent or
that are confounded with body weight
changes and/or other systemic toxicity
may be more difficult to interpret as  ,
neurotoxic effects.
  (a) Motor function: Neurotoxicants
commonly affect motor function. These
effects can be categorized generally into
(1) weakness or decreased strength, (2)
tremor; (3) Lncootdination, and (4)
spasms, myoclonia, or abnormal motor
                      movements (Tilson. 1987; Cory-Slechta.
                      1989). Specialized tests used to assess
                      weakness include- measures of grip
                      strength, swimming endurance.
                      suspension from a hanging rod. and
                      discriminative motor function. Rotarod
                      and gait assessments are used to
                      measure incoordination. while rating
                      scales and spectral analysis techniques
                      can be used to quantify tremor and other
                      abnormal movements.
                        (b) Sensory function: Gross
                      perturbations of sensory function can be
                      observed in simple neurological
                      assessments such as the FOB. However.
                      these tests may not be sufficiently
                      sensitive to detect subtle sensory
                      changes. Psychophysical procedures
                      that study the relationship between a
                      physical dimension (e.g.. intensity,
                      frequency) of a stimulus and behavior
                      may be necessary to quantify agent-
                      induced alterations in sensory function.
                      Examples of psychophysical procedures
include discriminated conditioning and
startle reflex modification.
  (c) Cognitive function: Alterations in
teaming and memory in experimental
anitnaU must be inferred from changes
in behavior following exposure when
compared with that either seen prior to
exposure or with a nonexposed control
group. Learning is defined as a
relatively lasting change in behavior due
to experience, and memory is defined as
the persistence of a teamed behavior
over time. Table 8 lists several examples
of learning and memory tests and
representative neurotoxicants known to
affect these tests.. Measurement of
changes in learning and memory must
be separated from other changes in
behavior that do not involve cognitive
or associative processes (i.e., motor
function, sensory capabilities.
motivational factors). In addition, any
apparent toxicant-induced change in
learning or memory should ideally be

-------
                Federal Register-/ VoL. 60.  N'o. 192  f Wednesday.  October 4, -\.gg&j Notices
                                                                    5204?
demonstrated avara range, of stimulus
and response conditions and testing
conditions. In developmental exposures.
it should be shown that the animals
have matured enough to perform the
specified task. Developmental
neurotoxicants can accelerate or delay
the ability to learn a response or
interfere with cognitive function at the
time of testing. Older animals frequently
perform- poorly on some types of tests,
and it must be demonstrated that
control animals in this population are
capable of performing the procedure.
Neurotoxicants might accelerate age-
related dysfunction or alter motivational
variables that are important for learning
to occur. Further, it is not necessarily
the case that a decrease in responding
on a learning task is adverse while an
increase in performance on a learning
task is not. It is well known that lesions
in certain regions of the brain can
facilitate the acquisition of certain types
of behaviors by removing preexisting
response tendencies (e.g., inhibitory
responses due to stress) that moderate
the rate of learning under normal
circumstances. Examples of learning
and memory procedures include simple
habituation, classical conditioning, and
operant (or instrumental) conditioning,
including tests for spatial learning and
memory.
   e. Developmental Neurotoxicity.
Although the previous discussion of
various neurotoxicity end points and
tests applies to studies  in which
developmental exposures are used.
there are particular issues, of importance
in the evaluation of developmental
neurotoxicity studies. Exposure to
chemicals during development can
result in a spectrum of effects, including
death, structural abnormalities, altered
growth, and functional deficits (U.S.
EPA, 1991b). Children are often
differentially sensitive  to chemical
exposure. A number of agents have been
shown to cause developmental
neurotoxicity when exposure occurred
during the period between conception
and sexual maturity (e.g., Riley and
Vorhees, 1988; Vorhees, 1987). Table 7
lists several examples of agents known
to produce developmental neurotoxicity
in experimental animals. Animal
models of developmental neurotoxicity
have been shown to be sensitive to
several environmental agents known to
produce developmental neurotoxicity in
humans, including lead, ethanol. x-
irradiation. methylmercury, and   .
polychlorinated biphenyls (PCBs)
(Kimmei et al.. 1990; Needleman. 1990:
Jacobson et al.. 1985; Needleman, 1988).
In many of these cases, functional
 deficits are observed at dose levels
beiownthosa:at.which other-indicators-of
developmental toxicity are evident or at
minimally toxic doses in adults. Such
effects may be transient, but generally
are considered to Be adverse effects.

        TABLE 7.—EXAMPLES OF
  DEVELOPMENTAL NEUROTOXICANTS
Alcohols .....
Antirmtotics-.

Insecticides
Metals  	
Poryhatogenated hy-
  drocarbons.
Solvents 		
Memanot, ethanof  •
X-fadatioo,       :
  azacytioine.
DDT.Jsepone.
LeaoV-methylmercury,
  cadmium.
PCSs, PBBs.

Carbon disurflde. tolu-
  ene^ '	..•'
  Testing for developmental"^ »"••: •  •
neurotoxicity has not been required-"'
routinely by regulatory agencies in the
United States, but is required by. the
EPA when other information indicates
the potential for developmental   .
neurotoxicity (U.S. EPA, 1988,1988a,
1988b, 1989.1991a. 1991b). Useful data
for decision making may be derived
from well-conducted adult
neurotoxicity studies, standard '
developmental toxicity studies, and
multigeneration studies; although the
dose levels used in the latter may be
lower than that in studies with shorter
term exposure.
  Important design issues to be -
evaluated for developmental
neurotoxicity studies are similar to
those for standard developmental
toxicity studies (e.g., a dose-response
approach with the highest dosa
producing minimal overt maternal or
perinatal toxicity. number of litters large
enough for adequate statistical power.
randomization of animals to dosa
groups and test groups, litter generally
considered as the statistical unit). In
addition, the us* of a replicate study
design provide* added confidence in the
interpretation of data. A
pharmacological/physiological
challenge may also be valuable in
evaluating neurologic function and
"unmasking" effects not otherwise
detectable. For example, a challenge
with a psychomotor stimulant such as
d-amphetamina may unmask latent
developmental neurotoxicity (Hughes
and Sparber. 1978; Adams and Buelke-
Sam. 1981; Buelke-Sam et al.. 1985).
   Direct extrapolation of developmental
neurotoxicity to humans is limited in
the same way as for other end points of
toxicity. i.e., by the lack of knowledge
about underlying lexicological
mechanisms and their significance (U.S.
EPA, 1991b). However, comparisons of
human and animal data for several
 agsnts known-to-cause developmental"'
 neurotoxicity in-humans showed many
 similarities in effects (Kimmei et al..
 1990). Comparisons at the level of
 functional category (sensory,
 motivational, cognitive, and motor
 function and social behavior) showed
 close agreement across species for the
 agents evaluated, even though the
 specific end-points used to assess these
 functions varied considerably across
 species (Stanton and Spear, 1990). Thus,
. it can be assumed that developmental
 neurotoxicity effects in animal studies
 indicate the potential for altered
 neurobehavioral development, in"n
 humans, although the specific types of  .
 developmental effects seen in  ''"  f
 experimental animal studies will nof"
 necessarily be the same as those that
 may be produced in humans. Therefore,
 when data suggesting adverse effects in
 developmental neurotoxicity studies are
 encountered for particular agents, they
 should be considered in the risk
 assessment process.
  Functional tests with a moderate
 degree of background variability, (e.g.. a
 coefficient of variability of 20 percent or
 less) may be more sensitive to the effects
 of an agent on behavioral end points
 than are tests with low variability that
 may be impossible to disrupt without
 using life^thraatening doses. A battery of
 functional tests, in contrast to a single
 test, is usually needed to evaluate the
 full complement of nervous system
 functions in an animal. Likewise, a
 series of tests conducted in animals in
 several age groups may provide more
 information about maturational changes
 and their persistence than tests
 conducted at a single age.
  It is a well-established principle that
 there are critical developmental periods
 for the disruption of functional
 competence, which include both the
 prenatal and postnatal periods to the
 time of sexual maturation, and the effect
 of a toxicant is likely to vary depending
 on the time and degree of exposure
 (Rodier. 1978.1990). It is also important
 to consider the data from studies in
 which postnatal exposure is included,
 as there may be an interaction of the
 agent with maternal behavior, milk.
 composition, pup suckling behavior, as
 well as possible direct exposure of pups
 via dosed food or water (Kimmei et al..
 1992).
  Agents that produce developmental
 neurotoxicity at a dose that is not toxic
 to the maternal animal are of special
 concern. However, adverse
 developmental effects are often
 produced at doses that cause maternal
 toxicity (e.g., <20 percent reduction in
 weight gain during gestation and
 lactation). In these cases, the

-------
52048
Federal  Register   Vol. 60. N'o.  192 / Wednesday-, October  4.  1995 / Notices
Developmental effects are still
Considered to represent neurotoxicity
and should not be discounted as being .
secondary to maternal toxicity. At doses
causing moderate maternal toxicity (i.e.,
>20 percent reduction in weight gain
during gestation and lactation),
interpretation of developmental effects
may be confounded. Current
information is inadequate to assume
that developmental effects at doses
causing minimal maternal toxicity result
only from maternal toxicity; rather, it
may bt that the mother and developing
organism are equally sensitive to that
doss level. Moreover, whether
developmental effects are secondary to •
maternal toxicity or not. the maternal
effects may be reversible while the
effects on the offspring may be
permanent. These are important
considerations for agents to which
humans may be exposed at minimally
toxic levels either voluntarily or
involuntarily, because several agents are
known to produce adverse
developmental effects at minimally
toxic doses in adult humans (e.g.,
alcohol) (Coles et al., 1991).
  Although interpretation of
developmental neurotoxicity data may
be limited, it is dear that functional
effects must be evaluated in light of
other toxicity data, including other
forms of developmental toxicity (e.g.,
structural abnormalities, perinatal
death, and growth retardation). For
example, alterations in motor
performance may be due to a skeletal
malformation rather than nervous
system change. Changes in learning
tasks that require a visual cue might be
influenced by structural abnormalities
in the eye. The level of confidence that
an agent produces an adverse effect may.
be as important as the type of change
seen, and confidence may be increased
by such factors as reproducibility of the
effect either in. another study of the
same function or by convergence of data.
from tests that purport to measure
similar functions-. A dose-response
relationship is an extremely important
measure of a chemical's effect; in the
case of developmental neurotoxicity
both monotonic and biphasic dose-
response curves are likely, depending
on the function being tested. The EPA
Guidelines for Developmental Toxicity
Risk Assessment (U.S. EPA, 1991b) may
be consulted for more information on
interpreting developmental toxicity
studies. The endpoints frequently used
to assess developmental neurotoxicity
in exposed children was recently
reviewed by Winneke (1995).
                      3. Other Considerations
                        a. Pharmacokinetics. Extrapolation of
                      test results between species can be
                      aided considerably by data on the
                      pharnracokinetics of a particular agent
                      in the species tested and. if possible, in
                      humans. Information on a toxicant's
                      half-life, metabolism, absorption.
                      excretion, and distribution to the
                      peripheral and central nervous system
                      may be useful in predicting risk. Of
                      particular importance for the
                      pharmacokinetics of neurotoxicants is
                      the blood-brain barrier, which
                      ordinarily excludes ionic and nonlipid
                      soluble chemicals from the central
                      nervous system. The brain contains
                      tircumventricular organs whose
                      purpose seems to be to sense the
                      chemical composition of the peripheral
                      circulation and activate mechanisms to
                      bring the composition of the blood back
                      to equilibrium if disturbed. These areas
                      are technically inside the brain, but they
                      lie outside of the blood-brain-barrier.
                      Therefore, chemicals from the periphery
                      can pass directly into the brain at these
                      sites. The majority of these structures
                      are located within or near the
                      hypothalamus, an area that is crucial for
                      maintenance of neuroendocrine
                      function. Phannacokinetic data may be
                      helpful in defining the dose-response
                      curve, developing a more accurate basis
                      for comparing species sensitivity
                      (including that of humans), determining
                      dosimetry at target sites, and comparing
                      phannacokinetic profiles for various
                      dosing regimens or routes of
                      administration. The correlation of
                      phannacokinetic parameters and
                      neurotoxicity data may be useful in
                      determining the contribution of specific
                      phannacokinetic processes to the effects
                      observed.
                        b. Comparisons of Molecular
                      Structure. Comparisons of the chemical
                      or physical properties of an agent with
                      those of known neurotoxicants may
                      provide some indication of the potential
                      for neurotoxicity. Such information may
                      be helpful for evaluating potential
                      toxicity when only minimal data are
                      available. The structure-activity
                      relationships (SAR) of some chemical •
                      classes have been studied, including
                      hexacarbons, organophosphates,
                      caroaraates, and pyrethroids. Therefore,
                      class relationships or SAR may help
                      predict neurotqxicity or interpret data
                      from neurotoxicological studies. Under
                      certain circumstances (e.g.. in the case
                      of new  chemicals), this procedure is one
                      of the primary methods used to evaluate
                      the potential for toxicity when little or
                      no empirical toxicity data are available.
                      It should be recognized, however, that
                      effects of chemicals in the same class
can vary widely. Moser (1994), for
example, reported that the behavioral
effects of prototypic cholinesterase-
inhibiting pesticides differed
qualitatively in a battery of behavioral
tests.
  c. Statistical Considerations. Properly
designed, studies on the neurotoxic
effects of compounds will include
appropriate statistical tests of
significance. In general, the likelihood
of obtaining a significant effect will
depend jointly on  the magnitude of the
effect and the variability obtained in
control and treated groups. A number of
texts are available  on standard statistical
tests (e.g.. Siegel, 1956; Winer, 1971;
Sokal and Rohlf, 1969; Salsburg. 1986:
Gad and Weil. 1988).
  Neurotoxicity data present some
unique features that must be considered
in selecting statistical tests for analysis.
Data may involve several different
measurement scales, including
categorical (affected or not), rank (more
or less affected), and interval and ratio
scales of measurement (affected by some
percentage). For example, convulsions
are usually recorded as being present or
absent (categorical), whereas
neuropathological changes are
frequently described in terms of the
degree of damage (rank). Many tests of
neurotoxicity involve interval or ratio
measurements (e.g., frequency of
photocell interruptions or amplitude of
an evoked potential), which are the
most powerful and sensitive scales of
measurement. In addition.
measurements are  frequently made
repeatedly in control and treated
subjects, especially in the case of
behavioral and neurophysiological end
points. For example, OPPTS guidelines
for FOB assessment call for evaluations
before exposure and at several times
during exposure in a subchronic study
(U.S. EPA. 1991a).
  Descriptive data (categorical) and rank
order data can be analyzed using
standard nonparametric techniques
(Siegel. 1956). In some cases, if it is
determined that the data fit the linear
model, the categorical modeling
procedure can be used for weighted
least;squares estimation of parameters
for a wide range of general linear
models, including  repeated-measures
analyses. The weighted least-squares
approach to categorical and rank data
allows computation of statistics for
testing the significance of sources of
variation as reflected by the model. In
the case of studies  assessing effects in
the same animals at several time points.
univariate analyses can Be carried out at
each time point when the overall dose
effect or the dose-by-time interaction is
significant.

-------
                 Federal  Register / Vol. 60. No.  192  /  Wednesday.  October  4. 1995  '  Nouces           52049
  Continuous data (e.g.. magnitude,
rate, amplitude), if found to be normally
distributed, can be analyzed with
general linear models using a grouping
factor of dose and. if necessary; repeated
measures across time (Winer, 1971).
Univariate analyses of dose, comparing •
dose groups to the control group at each
time point, are performed when there is
a significant overall dose effect or a
dose-by-time interaction. Post hoc
comparisons between control and
treatment groups can be made  following
tests for overall significance. In the case
of multiple end points within a series of
evaluations, some type of correction' for
multiple observations is warranted
(Winer, 1971).
   d. In Vitro Data in Neurotoxicology.
Methods and procedures that fall under
the general heading of short-term tests-
include an array of in vitro tests that
have been proposed as alternatives to
whole-animal tests (Goldberg and
Frazier, 1989). In vitro approaches use
animal or human cells, tissues, or
organs and maintain them in a nutritive
medium. Various typea of in vitro
 techniques produce data for evaluating
 potential and known neurotoxic
 substances, including primary cell
 cultures, cell Lines, and cloned cells.
 While such procedures are important in
 studying the mechanism of action of
 toxic agents, their use in hazard
 identification in human health risk  .
• assessment has not been explored to any
 great extent
   Data from in vitro procedures are
 generally based on simplified
 approaches that require less time to
 yield  information than do many in vivo
 techniques. However, in vitro methods
 generally do not take into account thft
 distribution of the toxicant in the body.
 die route of administration, or the
 metabolism of the substance. It also is
 difficult to extrapolate in vitro data to
 animal or human neurotoxicity end
 points, which include behavioral
 changes, motor disorders, sensory and
 perceptual disorders, lack of
 coordination, and learning deficits. In
 addition, data from in vitro tests cannot
 duplicate the complex neuronal
 circuitry characteristic of the intact
 animal.
    Many in vitro systems are now being
 evaluated for their ability to predict the
  neurotoxicity of various agents seen, in
  intact animals. This validation process
  requires'considerations in study design.
  including defined end points of toxicity
  and an understanding of how a test
  agent would bo handled in vitro as
  compared to the intact organism.
  Demonstrated neurotoxicity in vitro in
  the absence of in vivo data is suggestive
  but inadequate evidence of a neurotoxic
effect. In vivo data supported by in vitro
data enhance thVreliabiiity';pf the in
vivo results. -""S.y/   /-'^r*"'
B. -Dose-Response Evaluation
  Dose-response evaluation is a critical
part of hazard characterization and
involves the description of the dose
response relationship in the available
data. Human, studies covering a range of
exposures are rarely available and
therefore animal data are typically used:
for estimating exposure levels likely to
produce adverse effects in humans.
Evidence for a dose-response
relationship is an important criterion in
establishing a neurotoxic effect.
although this analysis may be limited
when based on standard studies using
three dose groups or fewer. The
evaluation of dose-response
relationships includes identifying
effective dose levels as well as doses
associated with no increase in incidence
of adverse effects when compared with
controls. Much of the focus is on
identifying die critical effect(s) observed
at the lowest-observed-adverse-effect-
level and  die-no-observed-adverse-
effect-level associated with that effect.
The NOAEL is defined as the highest' '
dose at which there is no statistically or
biologically significant increase in the
frequency of an adverse neurotoxic
effect when compared with the
appropriate control group in a data base-
characterized as having sufficient
evidence  for use in a risk assessment
(see section C). Although a threshold is
assumed for neurotoxic effects, the •
existence of a NOAEL in an animal
study does not prove or disprove the1
existence or level of a biological
 threshold. Alternatively, mathematical
 modeling of the dose-response
 relationship may be performed to
 determine a quantitative estimate of
 responses in the experimental range.
 This approach can be used to determine
 a BMD, which may be used in place of
 the NOAEL (Crump, 1994) (see Dose-
 Response Analysis. Section IV).
   In addition to identifying the NOAEL/
 LOAEL or BMD, the dose-response
 evaluation defines the range of doses
 that are neurotoxic for a given agent.
 species, route of exposure, and duration
 of exposure. In.addition to these
 considerations, pharmacokinetic factors
 and other aspects that might influence-
 comparisons with human exposure
 scenarios should be taken into account
 For example, dose-response curves may
 exhibit not only monotonic but also U-
 shaped or inverted U-shaped functions
 (Davis and Svendsgaard. 1990). Such
 curves are hypothesized to reflect
 multiple mechanisms of action, the
  presence of homeostatic mechanisms.
and/or activation of compensatory or
protective mechanisms. In addition to
considering the shape of the dose-
response curve, it should also be
recognized that neurotoxic effects vary
in terms of nature and severity across
dose or exposure level. At high levels of
exposure, frank lesions accompanied by
severe functional impairment may be
observed. Such effects are widely
accepted as adverse. At progressively
lower levels of exposure, however, the'
lesions may-become less severe and die
impairments less obvious. At levels of
exposure near the NOAEL and LOAEL,
the effects will often be mild, possibly
reversible, and inconsistently found. In
addition, the end points showing   / .
responses may be at levels of      .f
organization below the whole organism
(e.g., neurochemical or
electrophysiological end points). The •
adversity of such effects can be
contentious (e.g., choiinesterase
inhibition), yet it is such effects that are
likely to be the focus of risk assessment
decisions. To the extent possible, this
document provides-guidance on
determining the adversity of neurotoxic
effects. However, the identification  of a
critical adverse effect often requires
considerable professional judgment and.
should consider factors such as the
biological plausibility of the effect, the
evidence of a dose-effect continuum.
and the likelihood for progression of the
effect with continued exposure.

C. Characterization of the Health-
Related Data Base
.  This section describes a scheme for
characterizing the sufficiency of
evidence for neurotoxic effects. This  -
scheme defines two broad'categories:
sufficient and insufficient (Table 8).
Categorization is aimed at providing
certain criteria for the Agency to use to
define the minimum evidence necessary
to define hazards and to conduct dose-
response analyses. It does not address-
the issues related to characterization of
risk, which requires analysis of
 potential human exposures and their
 relation to potential hazards to estimate
 die risks of those hazards from
 anticipated or estimated exposures.
Table 8:—Characterization of the Health-
 Rtlattd Deiabue
 Sufficient Evidence
 .. The sufficient evidence category includes
 data that collectively provide enough
 information to judge whether or not a human
 neurotoxic hazard could exist This category
 may include both human and experimental
 animal evidence. .
 Sufficient Human Evidence
   This category includes agents for which
 there is sufficient evidence from

-------
 52050           Federal Register  /  Vol. 60,  No.  192  /  Wednesday, October 4.  1995  /  Notices
              studies, s g.. case control and
 toaort studies, to :udge that some aeurotoxic
 affect is associated with exposure. A case
 ienes in conjunction with other supporting
 evidence may also be judged "sufficient
 evidence." Epideraiologic and clinical case
 studies should discuss whether the observed
 affects can be considered biologically
 plausible in relation to chemical exposure.
 .Historically, much often has been made  of
 the notion of causality in epidemiologic
 studies. Causality is a more stringent
 criterion than association and has become a
 topic of scientific and philosophical debate.
 See Susser [1986], for example, for a
 discussion of inference in epidemiology.)
 Sufficient Experimental Animal Evidence/
 Limited or No Human Data
  This category includes agents for which
 there is sufficient evidence from
 experimental animal studies and/or limited
 human data to judge whether a potential
 ueurotoxic hazard may exist Generally.
 agents that have been tested according to
 current test guidelines would be included in
 this category. The minimum evidence
 necessary to Judge that a potential hazard
 exists would be data demonstrating an effect
 in a single appropriate, well-executed study
 In a single experimental animal species.
 whereas the minimum evidence needed to
 judge that a potential hazard does not exist
 would include data from appropriate, well-
 executed laboratory •"'"'•I studies that
 evaluated a variety of the potential
 manifestations of neuroxtoxicity and showed
 no effects at.doses that were at least
 minimally toxic. Information on
 pharmacokinetics. mechanisms, or known
 properties of the chemical class may also
 strengthen the evidence.,

 Insufficient Evidence
  This category includes agents for which
 there is less than the minimum evidence
 sufficient for identifying whether or not a
 nourotoxlc hazard exists, such as agents for
 which there are no data on neurotoxicity  oe
 agents with data bases from studies in
 animals or humans that are limited by study
 design or conduct (e.g., inadequate conduct
 or report of clinical signs )TMany general
 toxicity studies, for example, are considered
 insufficient in terms of the conduct of
 clinical neurobehAvioral observations or the
 number of samples taken for histopathology
 of the nervous system. Thus, a battery of
 negative toxicity studies with the**
 •shortcomings would be regarded as providing
 insufficient evidence of the lack of a
 neurotoxic effect of the test matariaL Further.
 most screening studies based on simple
 observations involving autonomic and motor
 function provide insufficient evaluation of
 many sensory or cognitive functions. Data,
 which by itself would likely fall in this
 category, would also include information on
 structure-activity relationships or data from
 in vitro tests. While such information would
 be insufficient by itself to proceed further in
 the assessment it could be used to support
 the need for additional testing.
  Data from all potentially relevant studies.
 whether indicative of potential hazard or not
 should be included in this characterization.
The primary sources of data are human
 studies and case reports, experimental
 animal studies, other supporting data, and in
 vitro and/or structure-activity relationship
 data. Because a complex interrelationship
 exists among study design, statistical
 analysis, and biological significance of the
 data, a great deal of scientific judgment.
 based on experience with neurotoxicity data
 and with the principles of study design and
 statistical analysis, is required to adequately
 evaluate the data base on neurotoxicity. In
 many cases, interaction with scientists in
 specific disciplines either within or outside.
 the field of neurotoxicology (e.g.,
 epidemiology, statistics) may be appropriate.
   The adverse nature of different
 neurotoxicity end points may be a complex
 judgment In general, most neuropathological
 and many neurooehavioral changes are
 regarded as adverse. However, there are
 adverse behavioral effects that may not
 reflect a direct action on the nervous system.
 Neurochemical and electrophysiological
 changes may be regarded as adverse as a
 function of their known or presumed relation
 to neuropathological and/or neurooehavioral
 consequences. In the absence of supportive
 information, a professional judgment must be
 made regarding the adversity of such
 outcomes, considering factors such as the
 nature, magnitude; and duration of the effects
 reported. Thus, correlated measures of
 neurotoxicity strengthen the evidence fix a
 hazard. Correlations between functional and
 morphological effects, such as the correlation
 between leg weakness and paralysis and
'peripheral nerve damage from exposure to
 tri-ortho-cresyl phosphate, an the most
 common and striking example of this form of
 validity. Correlations support a coherent and
 logical link between behavioral effects and
 biochemical mechanisms. Replication of &
 finding also strengthens the evidence for a
 hazard. Some neurotoxicants cause similar
 effects across most spades. Many chemicals
 shows to produce neurotoxicity in laboratory
 anim«l« have similar effects in humans.
 Some neurologic effects may be considered
 adverse even if they are small in magnitude.
 reversible, or the result of indirect
   Because of the inherent difficulty in
 "proving any negative." it is more difficult to
. document a finding of no apparent adverse
 effect than a finding of an adverse effect.
 Neurotoxic effects (and most kinds of
 toxicity) can be observed at many different
 levels, so that only a single end point needs
 to be found to demonstrate a hazard, but-
 many end points need to be examined to
 demonstrate no effect For example, to judge
 that a hazard for neurotoxicity could exist for
 a given agent, the minimum evidence
 sufficient would be data on a single adverse
 end point from a well-conducted study. In
 contrast, to judge that an agent is unlikely to
 pose a hazard for neurotoxicity, the
 minimum evidence would include data from
 a host of end points that revealed no
 neurotoxic effects. This may include human
 data from appropriate studies that could
 support a. conclusion of no evidence of a
 neurotoxic effect. With respect to clinical
 signs aad symptoms, human exposures can
 reveal rat more about the absence of effects.
 than animal studies, which are confined to
 the signs examined.
   in some cases, it may be that no individual
 study is judged sufficient to establish a
 hazard, but the total available data may
 support such a conclusion. Pharmacokinetic
 data and structure-activity considerations.
 data from other toxicity studies, as well as
 other factors may affect the strength of the
 evidence in these situations. For example,
 given that gamma diketones are known to
 cause motor system neurotoxicity, a marginal
 data.set on a candidate gamrna diketone, e.g.,
 Vio animals affected, might be more likely to
 be judged sufficient than equivalent data
 from a member of a chemical class about
 which  nothing is known.        ;
   A judgment that the toxicology data base
 is sufficient to indicate a potential neurotoxic
 hazard is not the end of analysis. The
 circumstances of expression of hazard are  *
 essential to describing human hazard     ,/
 potential Thus, reporting should contain tpe
 details of the circumstances under which
 effects  have been observed, e.g.. "long-term
 oral exposures of adult rodents to compound
 X at levels of roughly 1 rag/kg have been
 associated with ataxia and peripheral nerve
 damage."

 IV. Dose-Response Analysis
   This section describes several
 approaches (including the LOAEL/
 NOAEL and BMD) for determining tha
 reference dose or reference
 concentration. The NOAEL or BMD/
 uncertainty factor approach results in a
 RfD or RfC. which is an estimate (with
 uncertainty spanning perhaps an order
 of magnitude) of a daily exposure to the
 human population (including sensitive
 subgroups) that is likely to be without
 an appreciable risk of deleterious effects
 during a lifetime.
  The dose-response analysis
characterization should:
  a. Describe how the RfD/RfC was
calculated:
  b. Discuss the confidence in the
estimates;
  c. Describe the assumptions or
uncertainty factors used; and
  d. Discuss the route and level of
exposure  observed, as compared to
expected human exposures.
(Specifically, are the available data from
the same route of exposure as the
expected human exposures? How many
orders of magnitude do you need to
extrapolate from the observed data to
environmental exposures?)

A. LOAEUNOAEL and Benchmark Dose
(BMD) Determination
  As indicated earlier, the LOAEL and
NOAEL are determined for endpoints
that are seen at the lowest dose level
(so-called critical effect). Several
Limitations in the use of the NOAEL
have been identified and described (e.g.,
Barnes and Dourson. 1986; Crump,
1984).  For example, the NOAEL is
derived from a single end point from a
single study (the critical study) and

-------
                   Federal Register / Vol. 60. No. 192 V  Wednesday. October 4.  1995
                                                  /  Notices
                                                                     52051
  ignores both the slope of the dose-
  response function and baseline
  variability in the end point of concern.
  Because the baseline variability is not
  taken into account, the NOAEL from a
  study using small group sizes may be
  higher than the NOAEL from a similar-
  study in the same species that uses
  larger group sizes. The NOAEL is also
  directly dependent on the dose spacing
  used in the study. Finally, and perhaps
  most importantly, use of the NOAEL
  does not allow estimates of risk or
  extrapolation of risk to lower dose
  levels.
    Because of these and other limitations
  in the NOAEL approach, mathematical
  curve-fitting techniques (Crump, 1984:
  Gaylor and Slikker, 1990; Glowa. 1991;
  U.S. EPA, 1995a) are beginning to be
  used with, or as an alternative to, the
  NOAEL in calculating the RfD or RfC.
  The Agency is in the process of
  implementing these newer techniques  •
  and strongly encourages the calculation
  of BMDs for neurotoxicity and other
  health effect end points. These-
  techniques typically apply a
  mathematical function that describes
  the dose-response relationship and then
  interpolate to a level of exposure
  associated with a small increase in
  effect over that occurring in the control
  group or under baseline conditions. The
  BMD has been defined as a lower
  confidence limit on the effective dose
  associated with some defined level of
  effect, e.g., a 5 percent or 10 percent
  increase in response (i.e., a BMDos or
  BMDio for a particular effect). Because
  the model is only used to interpolate
  within the dose range of the study, no
  assumptions about the existence (or
  nonexistence) of a threshold are needed.
 Thus, any model that fits the data well
 is likely to provide a reasonable
 estimate-of the BMD.
   Many neurotoxic end points provide
 continuous measures of response, such
 as  response speed, nerve conduction
 velocity, IQ score, degree of enzyme
 inhibition, or the accuracy of task
 performance. Although it is possible to
 impose a dichotomy on a continuous
 effects distribution and to classify some
 level of response as "affected" and the
 remainder as "unaffected," it may be
 very difficult and inappropriate to
 establish such dear distinctions,
' because such a dichotomy would
 misrepresent the true nature  of the
 neurotoxic response. Alternatively.
 quantitative models designed to analyze
 continuous effect variables may be
 preferable. Other techniques that allow
 this approach, with transformation of
 the information into estimates of the
 incidence or frequency of affected
 individuals in a population, have been
  proposed (Cnup|,, 1984;,'G^,ylor and
  Slikker. 1990).'Ga'tegorical*regression
  analysis has been;pr6posed since it can
  evaluate different types of data and
  derive estimates for short-term
  exposures (Rees and Hattis, 1994).
  Decisions about the most appropriate
  approach require professional judgment,
  taking into account the biological nature
  of the continuous effect variable and its
  distribution in the population under
  study.
   Although dose-response functions in
 neurotoxicology are generally linear or
  monotonic. curvilinear functions,
  especially U-shaped or inverted U-
  shaped curves, have been reported as
  noted earlier (Section ffl B). Dose-
 response analyses should consider  the
 uncertainty that U-shaped dose-
 response functions might contribute to
 the estimate of the NOAEL/LOAEL or
 BMD. Typically, estimates of the
 NOAEL/LOAEL are taken from the
 lowest part of the dose-response curve
 associated with impaired function or
 adverse effect.

 B. Determination of the Reference Dose
 or Reference Concentration
   Since the availability of dose-response
 data in humans is limited,  extrapolation
 of data from «nimq|§ to humans usually
 involves the application of uncertainty
 factors to the NOAEL/LOAEL or BMD.
 The NOAEL or BMD/uncertainty factor
 approach results in a RfD or RfC, which
 is an estimate (with uncertainty
 spanning perhaps an order of
 magnitude) of a daily exposure to the
 human population (including sensitive
 subgroups) that is likely to be without
 an appreciable risk of deleterious effects
 during a lifetime. The oral RfD and
 inhalation RfC are applicable to chronic
 exposure situations and are based on an
 evaluation of all the noncancor health
 effects, including neurotoxicity data.
 RfDs and RfC« in the Integrated Risk
 Information System (IRIS-2) data base
 for several agents are based on
 neurotoxicity end points and include a
 few cases in which the RfD or RfC is
 calculated using the BMD approach
 (e.g., methylmercury, carbon disulfide).
 The size of the final uncertainty factor
 used will vary from agent to agent and
 will require the exercise of scientific
judgment, taking into account
 intersperies differences, the shape of the
dose-response curve, and the
neurotoxicity end points observed.
Default uncertainty factors are typically
multiples of 10 and ate used to
compensate for human variability in
sensitivity, the need to extrapolate from
animals to humans, and the need to
extrapolate from less than lifetime (e.g.,
subchronic) to lifetime exposures. An
  additional factor of up to 10 may be
  included when only a LOAEL (and not
  a NOAEL) is available from a study, or
  depending on the completeness of the
  data base, a modifying factor of up to 10
  may be applied, depending on the
  confidence one has in the data base.  -.
  Barnes and Dourson (1988) provide a
  more complete description of the
  calculation, use. and significance  of
  RfDs in-setting exposure limits to  toxic
  agents by the oral route. Jarabek et al.
  (1990) provide a more complete
  description of the calculation, use, and
  significance of RfCs in setting exposure
  limits to toxic agents in air.
  Neurotoxicity can result from acutefc
  shorter term exposures, and it may/be
  appropriate in some cases, e.g., for air
  pollutants or water contaminants,  to set
  shorter term exposure limits for
  neurotoxicity as well as for other
  noncancer health effects.

  V. Exposure Assessment
   Exposure assessment describes the
  magnitude, duration, frequency, and
  routes of exposure to the agent of '•
  interest. This information may come
  from hypothetical values, models,  or
 actual experimental values, including
 ambient environmental sampling
 results. Guidelines for exposure
 assessment have been published
 sepa-ately (U.S.  EPA. 1992) and will.
 therefore, be discussed only briefly here.
   The exposure assessment should
 include an exposure characterization  '
 that:
   a. Provides a statement of the
 purpose, scope, level of detail, and.
 approach used in the exposure
 assessment:
   b. Presents the estimates of exposure
 and dose by pathway and route for
 individuals, population segments, and
 populations in a manner appropriate for
 the intended risk characterization;
   c. Provides an evaluation of the
 overall level of confidence in the
 estimate of exposure and dose and the
 conclusions drawn; and
   d. Communicates the results of the
 exposure assessment to the risk
 assessor, who can then use the exposure
 characterization, along with the
 characterization of the other risk
 assessment elements, to develop a risk
 characterization.
  A number of considerations are
 relevant to exposure assessment for
 neurotoxicants. An appropriate
evaluation of exposure should consider
the potential for exposure via ingestion,
inhalation, and dermal penetration from
relevant sources of exposures, including
multiple avenues of intake from the
same source. On-going Agency activities
that support neurotoxicity exposure

-------
32052
Federal  Register    Vol.  60.  Mo. 192  /  Wednesday.  October 4. 1995 / N'otices
assessment include characterizing
cumulative nsk and revising the
Guidelines for the Health Risk
Assessment of Chemical Mixtures.
  In addition, neurotoxic effects may
result from short-term (acute), high-
concentration exposures as well as from
longer term (subchronic), lower level
exposures. Neurotoxic effects may-occur
after a period of time  following initial
exposure or be obfuscated by repair
mechanisms or apparent tolerance. The
type and severity of effect may depend
significantly on the pattern of exposure
rather t.h«n on the average dose over a
long period of time. For this reason,
exposure assessments for neurotoxicants
may be much more complicated than
those for long-latency effects such as
carcinogenicity. It is rare for sufficient
data to be available to construct such
patterns of exposure or dose, and
professional judgment may be necessary
to evaluate exposure to neurotoxic
agents.
VI. Risk Characterization

A. Overview
  Risk characterization, the culmination
of the risk assessment process, consists
of an integrative analysis and a risk
characterization summary. The
integrative analysis (a) involves
integration of the toxicity information
from the hazard characterization and
dose-response analysis with the human
exposure estimates, (b) provides an
evaluation of the overall quality of the
assessment and the degree of confidence
in the estimates of risk and conclusions
drawn, and (c) describes risk in terms of
the nature and extent of harm. The risk
characterization summary
communicates the results of the risk
assessment to the risk manager.
  This summary should include but is
not limited to a discussion of the
following elements:
  a. Quality of and confidence in the
available data;
  b. Uncertainty analysis;
  c. Justification of defaults or
assumptions;
  d. Related research recommendations:
  e. Contentious issues and extent of
scientific consensus;
  f. Effect of reasonable alternative
assumptions on conclusions and
estimates:
  g. Highlight reasonable plausible
ranges;
  h. Reasonable alternative models; and
  i. Perspective through analogy.
  The risk manager can then use the
risk assessment, along with other risk
management elements, to make public
health decisions.
  An effective risk characterization
must  fully, openly, and clearly
                     characterize risks and disclose the
                     scientific analyses, uncertainties.
                     assumptions, and science policies that
                     underlie decisions throughout the risk
                     assessment and risk management
                     processes. The risk characterization
                     must feature values such as
                     transparency in the decision-making
                     process; clarity in communicating with
                     each other and the public regarding
                     environmental risk and the  '
                     uncertainties associated with
                     assessments of environmental risk; and
                     consistency across program offices in
                     core assumptions and science policies.
                     which are well grounded in science and
                     reasonable.
                       The following sections describe these
                     four aspects of die risk characterization
                     in more detail.

                     B. Integration of Hazard
                     Characterization, Dose-Response
                     Analysis and Exposure Assessment
                       In developing the hazard
                     characterization, dose-response analysis
                     and exposure portions of the risk
                     assessment, the assessor must take into
                     account many judgments concerning
                     human relevance of the toxicity data.
                     including the appropriateness of the
                     various animal models for which data
                     are available and the route, timing, and
                     duration of exposure relative to
                     expected human exposure. These
                     judgments should be summarized at
                     each stage of the risk assessment process
                     (e.g., the biological relevance of
                     anatomical variations may be
                     established in the hazard
                     characterization process, or the
                     influence of species differences in
                     metabolic patterns in the dose-response
                     analysis). In integrating the information
                     from the assessment the risk assessor
                     must determine if some of these
                     judgments have implications for other
                     portions of the assessment and whether
                     the various components of the
                     assessment are compatible.
                       The risk characterization should not
                     only examine the judgments but also
                     explain the constraints of available data
                     and the state of knowledge about the
                     phenomena studied in making them.
                     including (1} the qualitative conclusions
                     about the likelihood that the chemical
                     may pose a specific hazard to human
                     health, the nature of the observed
                     effects, under what conditions (route,
                     dose levels, time, and duration} of
                     .exposure these effects occur, and
                     whether the health-related data are
                     sufficient to use in a risk assessment; (2)
                     a discussion of the dose-response
                     characteristics of the critical effects(s),
                     data such as the shapes and slopes of
                     the dose-response curves for the various
                     end points, the rationale behind the
determination of the NOAEL and
LOAEL and calculation of the
benchmark dose, and the assumptions
underlying the estimation of the RfD or
RfC; and (3) the estimates of the
magnitude of human exposure; the
route, duration, and pattern of the
exposure; relevant pharmacokinetics:
and the number and characteristics of
the population(s) exposed.
  If data to be used in a risk
characterization are from a route of
exposure other >b«" the expected
human exposure, then pharmacokinetic
data should be used, if available, to
make extrapolations across routes of
exposure. If such data are not available, 4
the Agency makes certain assumptions/
concerning, the amount of absorption  y
likely or the applicability of the data
from one route to another (U.S. EPA.
1992).
  The level of confidence in the hazard
characterization should bo stated to  the
extent possible, including the
appropriate category regarding
sufficiency of the health-related data. A
comprehensive risk assessment ideally
includes information on a variety of end
points that provide insight into the full
spectrum of potential neurotoxicological
responses. A profile that integrates both
human and test species data and
incorporates a broad range of potential
adverse neurotoxic effects provides
more confidence in a risk assessment for
a given agent
  The ability to describe the nature of
the potential human exposure is
important to predict when certain
outcomes can be anticipated and the •
likelihood  of permanence or
reversibility of the effect An important
part of this effort is a description of the
nature of the exposed population and
the potential for sensitive, highly
susceptible, or highly exposed
populations. For example, the
consequences of exposure to the
developing individual versus the adult
can differ markedly and can influence
whether the effects are transient or
permanent Other considerations
relative to human exposures might
include the likelihood -of exposures  to
other agents, concurrent disease, and
nutritional status.
  The presentation of the integrated
results of the assessment should* draw
from and highlight key points of the
individual characterizations of
component analyses performed under
these Guidelines. The overall risk
characterization represents the
integration of these component
characterizations. If relevant risk
assessments on the agent or an
analogous agent have been done by EPA
or other Federal agencies, these should

-------
                  Federal Register / Vol. 60. Mo.  192; / Wednesday. October  4.  1995 / Notices          52053
 be described and the similarities and
 differences discussed.

 C. Quality of the Data Base and Degree
 of Confidence in the Assessment

   The risk characterization should
 summarize the kinds of data brought
 together in the analysis and the
 reasoning on. which the assessment is
 based. The description should convey
 the major strengths and weaknesses of
 the assessment that arise from
 availability of data and the current
 limits of our understanding of the
 mechanisms of toxicity.
   Health risk is a function of the hazard
 characterization, dose-response
 analysis, and exposure assessment.
 Confidence in the results of a risk
 assessment is, thus, a function of
 confidence in the results of the analysis
 of these elements. Each of these
 elements should have its own
 characterization as a part of the
 assessment Within each
 characterization, the important
 uncertainties of the analysis and
 interpretation of data should be
 explained, and the risk manager should
 be given a dear picture of consensus or
 lack of consensus that exists about -
 significant aspects of the assessment.
 Whenever more »h»" one view is  •
 supported by the data and choosing
 between them is difficult, all views
 should be presented. If one has been
 selected over the others, the rationale
 should be given; if not. then all should
 be presented as plausible alternative
 results.

 D. Descriptors of Neurotoxicity Risk

   There are a number of ways to
. describe risks. Several ways that are
 relevant to describing risks for
 neurotoxicity are as follows:

 1. Estimation of the Number of
 Individuals

   The RfD or RfC is taken to be a
 chronic exposure level at or below
 which no significant risk occurs.
 Therefore, presentation of th»
 population in terms of those at or below
 the  RfD or RfC ("not at risk") and above
 the  RfD or RfC ("may be at risk") may
 be useful information for risk managers.
 This method is particularly useful to a
 risk manager considering possible
 actions to ameliorate risk for a
 population. If the number of persons in
 the  at-risk category can be estimated.
 then the number of persons removed
 from the at-risk category after a
 contemplated action is taken can be
 used as an indication of the efficacy of
 the  action.
2. Presentation of Specific Scenarios
               '        '
            ,    --.     -.»
  Presenting specific scenarios in the
form of "what if?" questions is
particularly useful to give perspective to
the risk manager, especially where
criteria, tolerance limits, or media
quality limits are being set The
question being asked in these cases is,  .
at this proposed limit, what would be
the resulting risk for neurotoxicity
above the RfD or RfC?

3. Risk Characterization for Highly
Exposed Individuals
  This  measure is one example of the
just-discussed descriptor. This measure
describes the magnitude of concern at
the upper end of the exposure
distribution. This allows risk managers
to evaluate whether certain individuals
are at disproportionately high or
unacceptably high risk.
  The objective of looking at the upper
end of the exposure distribution is to
derive a realistic estimate of a relatively
highly exposed individual or
individuals. This measure could be
addressed by identifying a specified
upper percentile of exposure in the
population and/or by estimating the
exposure of the highest exposed
individual(s). Whenever possible, it is
important to express the number of
individuals who comprise the selected
highly exposed group and discuss the.
potential tor exposure' at still higher
levels.
  If population data are absent, it will
often be possible to describe a scenario
representingjiigh-end exposures using
upper percentile or judgment-based
values for exposure variables. In these
instances caution should be used not to
compound a substantial number of high-
end values for variables if a
"reasonable** exposure estimate is to be
achieved.
4. Risk Characterization for Highly
Sensitive or Susceptible Individuals
  This  measure identifies populations
sensitive or susceptible to the effect of
concern. Sensitive or susceptible
individuals are those within the
exposed population at increased risk of
expressing the toxic effect All stages of
nervous system maturation might be
considered highly sensitive or
susceptible, but certain subpopulations
can sometimes be identified because of
critical periods for exposure, for
example, pregnant or lactatmg women,
infants, children.
  In general, not enough is understood
about the mechanisms of tbxicity to
identify sensitive subgroups for all
agents, although factors such as
nutrition, personal habits (e.g.. smoking.
 alcohol consumption, illicit drug abuse),
 or preexisting disease (e.g.. diabetes,
 sexually transmitted diseases) may
 predispose some individuals to be more
 sensitive to the neurotoxic effects of
 various agents.
 5. Other Risk Descriptors
   In risk characterization, dose-response
 information and the human exposure
 estimates may be combined either by
 comparing the RfD or RfC and the
 human exposure estimate or by
 calculating the margin of exposure
_ (MOE). The MOE is the ratio of the
 NOAEL from the most appropriate or
 sensitive species to the estimated
 human exposure level. If a NOAEL^s
 not available, a LOAEL may be used in •
 calculating the MOE Alternative! jTa
 benchmark dose may be compared with
 the estimated human exposure level to
 obtain the MOE. Considerations for  the
 evaluation of the MOE are similar to
 those for the uncertainty factor applied
 to the LOAEL/NOAEL or the benchmark
 dose. The MOE is presented along with
 a discussion of the adequacy of the data
 base, including the nature and quality of
 the hazard and exposure data, the
 number of species affected, and the
 dose-response information.
   The RfD or RfC comparison with the
 human exposure estimate and the
 calculation of the MOE are conceptually
 similar but are used in different
 regulatory situations. The choice of
 approach depends on  several factors.
 including the statute involved, the
 situation being addressed, the data base
 used, and the needs of the decision
 maker. The RfD or RfC and the MOE are
 considered along with other risk
 assessment and risk management issues
 in making risk management decisions.
 but the scientific issues that must be
 taken into account in establishing them
 have been addressed here.
   If the MOE is equal to or more than
 the uncertainty factor x any modifying
 factor used as a basis for an RfD or RfC.
 then the need for regulatory concern is
 likely to be small. Although these
 methods of describing risk do not
 actually estimate risks per se, they give
 the risk manager some sense of how
 close the exposures are to levels of
 concern.
 E. Communicating Results
   Once the risk characterization is
 completed, the focus turns to
 communicating results to the risk
 manager. The risk manager uses the
 results of the risk characterization along
 with other technological, social, and
 economic considerations in reaching a
 regulatory decision. Because of the way
 in which these risk management factors

-------
52054
Federal Register <  Vol.  60, No. 192 / Wednesday. October 4,  1995  /  Notices
may affect different cases, consistent but
not necessarily identical risk
management decisions must be made on
a case-by-case basis. These Guidelines
are not intended to give guidance on the
nonscientific aspects of risk
management decisions.

F. Summary and Research Needs

  These Guidelines summarize the-
procadures that the U.S. Environmental
Protection Agency would'use in
evaluating the potential for agents to
cause neurotoxicity. These Guidelines   .
discuss the general default assumptions
that should be made in risk assessment
for neurotoxicity because of gaps in our
knowledge about underlying biological
processes and how these compare across
species. Research to improve the risk
assessment process is needed in a
number of areas. For example, research
is needed to delineate the mechanisms
of neurotoxicity and pathogenesis.
provide comparative pharmacokinetic
data, examine the validity of short-term
in vivo and in vitro tests, elucidate the
functional modalities  that may be
altered, develop improved animal
models to examine the neurotoxic
effects of exposure during the premating
and early postmating periods and in
neonates, further evaluate the
relationship between maternal and
developmental toxitity, provide insight
into the concept of threshold, develop
approaches for improved mathematical
modeling of neurotoxic effects, improve
animal models for examining the effects
of agents given by various routes of
exposure, and address the synergistic or
antagonistic effects of mixtures of
chemicals and neurotoxic response.
Such research will aid in the evaluation
and interpretation of data on
neurotoxicity and should provide
methods to assess risk more precisely.

VH. Rsfsnocs*
Adams. J.: Buelke-Sam. J. (1931) Behavioral
    testing of tin postnatal animate tasting
    and methods development In: KlnunaL
    C.A.: Bualke-Sam, J.. eds. Developmental
    toxicology. New York: Raven Press, pp.
    233-238.
Anger. W.K. (1984) Neurobehavioral testing
    of chemicals: impact on recommended
    standards. Neurobehav. ToxicoL Teratol.
    6:147-153.
Anger. W.K. (1986) Workplace exposure*. In:
    Anntu. Z.A. ed., Neurobebavioral
    toxicology. Baltimore: John* Hopkins
    University Press, pp. 331-347_
Anger. W.K. (1990) Worksite behavioral
    research: results, sensitive methods, test
    batteries, and the transition from
    laboratory data to human health.
    Neurotoxicology 11:627-718.
                        Anger. K.: Johnson. B.L. (1985) Chemicals
                           affecting behavior. In: OTDonoghue, J..
                           ed. Neurotoxicity of industrial and
                           commercial chemicals. Boca Raton, FL:
                           CSC Press.
                        Barnes, D.G.: Dourson, M. (1988) Reference
                           dose (RfD): description and use in health
                           risk assessments. ReguL ToxicoL
                           PharmacoL 8:471-486.
                        Bondy, S.C. (1986) The biochemical
                           evaluation of neurotoxic damage.
                           Fundam. AppL ToxicoL 6:208-216.
                        Boyes. W.K. (1992) Testing visual system
                           toxicity using visual evoked potential
                           technology. In: Isaacson, R.L.; Jensen.
                       '   K.F., eds. The vulnerable brain and
                           environmental risks. VoL 1: Malnutrition
                           and hazard assessment New York:
                           Plenum, pp. 193—222.
                        Boyes. W.K. (1993) Sensory-evoked
                           potentials: measures of neurotoxicity. In:
                           Erinoff. L., ed. Assessing the tenacity of
                           drugs of abuse. NTDA Research
                           Monograph 136. National Institute on
                           Drug Abuse. Alcohol. Drug Abuse and
                           Mental Health Administration, U.S.
                           Department of Health and Human
                           Services, pp. 63-100.
                        Buelke-Sam. J.. Kimmel, C-A.; Adams. J.
                           (1985) Design considerations in
                           screening for behavioral teratogens:
                           result* of the collaborative teratology
                           study. Neurobehav. ToxicoL TeratoL
                           7:537-589.
                        Callender, T.J.; Morrow. U; Subnmaaian. K.
                           (1994) Evaluation of chronic
                           neurological sequelae after acute
                           pesticide exposure using SPECT brain
                           scans. J. ToxicoL Environ. HUh. 41:275-
                           284.
                        Carson, B.L.; Stockton. R.A.; Wilkinson. R.R.
                           (1987) Organomercury. lead, tin
                           compounds in the environment and the
                           potential for human exposure. In: Tllson.
                           H.A.;  Sparber. S.B.. eds. Neurotoxicants
                           and neurobiological function: effects of
                           organoheavy metals. New York: J. Wiley,
                           pp. 1-80.
                        Coles. CO.; Brown. R.T.: Smith, LB.;
                           Platrman. K-A.; Erickson. S.: Falek. A.
                           (1991) Effects of prenatal alcohol
                           exposure at school age I. Physical and'
                           cognitive development NeurotDXtcoL
                           TentoL 13:357-367.
                        Cory-Slechm. D.A. (1988) Behavioral
                           measures of neurotoxicity.
                           Neurotoxicology 10:271-298.
                        Costa. L.G. (1988) Interactions of
                           neurotcodcants with neurotransmittar
                           systems. Toxicology 49:359-366.
                        Crump. K.S. (1984) A new method for
                           determining allowable daily intakes.
                           Fundam. AppL ToxicoL 4:854-871.
                        Davis. J.M; Svendsgaard. D.J. (1990) U--
                           shaped dose-response curves: their
                           occurrence and implication for risk.
                           assessment J. ToxicoL Environ. Health
                           30:71-83.
                        Dyer. R.S. (1985) The use of sensory evoked
                           potentials in toxicology.  Fundam. AppL
                           ToxicoL 5:24-40.
Dyer. R.S. (1987) Macrophysiological
    assessment of organometal neurotoxicity.
    In: Tilson, H.A.; Sparber, S.B., eds.
    Neurotoxicants and neurobiological
    function effects of organoheavy metals.
    New York: J. Wiley, pp. 137-184.
Eccles. C.U. (1988) EEC correlates of
    neurotoxicity. Neurotoxicol. TermtoL
    10:423-428.
Ecobichon. D.J.; Joy, R.M. (1982) Pesticides
    and neurological diseases. Boca Raton.
    FL: CRC Press, pp. 151-203.
Ecobichon. D.J.; Davies. J.E.: Doull, J.; Ehrich.
    M.; Joy. R.; McMillan. D.; MacPhafl, R.;
    Reiter. L.W.; Slikker. W., Jr.; Tilson, H.
    (1990) Neurotoxic effects of pesticides.
    In: Baker. S.R.; Wilkinson. CF.. eds. The
    effect of pesticides on human health.      •>
    Princeton. NJ: Princeton Scientific       /
    Publishing Co., Inc., pp. 131-199.      
-------
                   Federal Register  /Vol. 60.  N'o- 192 '   Wednesday,  October  4.  1995     N'oc:c=o
                                                                            32055
Kjmrae!. C.A . Sees. 3.C.. Francis. E.Z.. eds.
    (19901 Qualitative and quantitative
    comparability of human and animal
    developmental aeurotoxicity.
    Neurotoxicol. Teratol. 12:175-292.
Kimmel, C.A.: Kavlock. R.J.; Francis, E.Z.
    (1992) Animal models for assessing
    developmental toxicity. In: Guzelian.
    P.S.: Henry. C.J.; Olin. S.S. eds.
    Similarities and differences between
    children and adults: implications for risk
    assessment. Washington. DC: ILSI Press,
    pp. 43-65.
Krinke, GJ. (1989) Neuropathologic
    screening in rodent and other species. J.
    Am. Coll. Toxicol. 8:141-155.
Last. J.M. (1986) Epidemiology and health
    information. In: Last. J.M.. ed. Maxcy-
    Rosenau public health and prevention
    medicine. New York; Appleton-Century-
    Crofts.
MacPhail, R.C (1985) Effects of pesticides on
    schedule-controlled behavior. In: Seiden,
    L.S.; Balster, R.L. eds. Behavioral
    pharmacology: the current status. New
    York: A.R. Liss, pp. 519-535.
MacPhail. R.C.; Peele. D.B.: Crofton. K.M.
    (1989) Motor activity and screening for
    neurotoxicity. J. Am. Coll. ToxicoL
    8:117-125.
Mailman. R.B. (1987) Mechanisms of CNS
    injury in behavioral dysfunction.
    NeurotoxicoL Teratol. 9:417-426.
Mattsson. J.L.: Albee, R.R. (1992) Sensory
    evoked potentials in neurotoxicology.
    NeurotoxicoL TeratoL 10:435-443.
Mattsson. J.L.; Boyes, W.K.; Ross. J.F. (1992)
    Incorporating evoked potentials into
    neurotoxicity test schemes. In: Tilson,
    H.A.: Mitchell. C.L.. eds. Target organ
    toxicology series: neurotoxicology. New
    York: Raven Press Ltd.. pp. 125-145.
Mausner, J.S.; Kramer. S. (198S)
    Epidemiology—an introductory text. 2nd
    ed. Philadelphia: W.B. Saunders.
Morell. P.: Mailman. R.B. (1987) Selective
    and nonselective effects of organometals
    on brain nmirochemistry. In: Tilson.
    H.A.; Sparber. S.B.. eds. Neurotoxicants
    and neurobiological function: effects of
    organoheavy metals. New York: Wiley,
    pp. 201-230.
Moser. V.C (1989) Screening approaches to
    neurotoxicity: a functional observational
    battery. ]. Am. ColL ToxicoL 8:85-93.
Moser, V.C (1994) Comparisons of th« acute
    effects of cholinasterase inhibitors using
    a neurobehavioral screening battery'in
    rats. The Toxicologist 14:241.
National Research Council (NBC). (1983) Risk
    assessment in the federal government
    Managing the process. Washington, DC:
    National Academy of Sciences.
National Research Council (NRC). (1984)
    Toxicity testing: strategies to determine
    needs and priorities. Washington. DO
    National Academy of Sciences.
National Research Council (NRQ. (1994)
    Science and judgment in risk
    assessment Washington. DO National
    Academy of Sciences.
National Resources Defense Council (NRDQ.
    (1989) Intolerable risk: pesticides in our
    children's food. New York: Natural
    Resources Defense Council.
Needleman. H. (1986) Epideraiolog'cal
    studies:'!/!: Annau: Z.A.. ed.
    Neuroljejiavioraybipcology. Baltimore:
    Johns Hopkins University Press, pp.
    279-287,;      :  %
Needleman. H.L. (1990) Lessons from the
    history of childhood plumbism for
    pediatric neurotoxicology. In: Johnson.
    B.L.: Anger. W.K.; Durao. A.; Xintaris, C.
    eds. Advances in neurobehavioral
    toxicology: application in environmental
   • and occupational health. Chelsea, MI:
    Lewis Publishers, Inc., pp. 331-337.
O'Callaghan. J.P. (1988) Neurotypic and
    gliotypic proteins as biochemical
    markers of neurotoxicity. NeurotoxicoL
    TeratoL 10:445-452.
OTtonoghue, J.L. (1989) Screening for
    neurotoxicity using a neurologically
    based examination and neuropathology.
    J. Am. ColL ToxicoL 8:97-115.
Office of Technology Assessment (OTA).
    (1990) Neurotoxicity: identifying and
    controlling poisons of the nervous
    system. U.S. Congress. Office of
    Technology Assessment (OTA-BA—436).
    Washington. DO U.S. Government
    Printing Office.
Omerand. I.E.: Harding. A.E.; Miller. D.H.:
    Johnson. G.; MacManus, D.. duBoulay,
    E.P.G.H.; Kendall. B.E.; Moseley. LF.;
    McDonald. W.L (1994) Magnetic
    resonance imaging in degenerative atoxic
    disorders. J. NeuroL Neurosurg.
    Psychiatry. 57:31-57.
Robert CS. (1983) Multisensory evoked
    potentials in experimental and applied .
    neurotoxicology. Neurooehav. ToxicoL
    TeratoL 5:659-8*1.
Reiter. UW. (1987) Neurotoxicology in
    regulation and risk assessment Dev.
    PharmacoL Ther. 10-454-368.
Rees, D.O; Hattis, D. (1994) Developing
    quantitative stntegim for animal to
    human extrapolation. In: Hayes, A.W.,
    ed.  Principles and ""*t«HlT of
    toxicology, 3rd ad. New York: Raven
    Press, pp. 275-315.
Reuhl. K.R. (1991) Delayed expression of
    neurotoxicity: the problem of silent
    rf«m«g«. NeurotoxicoL 12:341-346.
Rice. D.O (1988) Quantification of operant
    behavior. ToxicoL Lett 43:361-379.
Riley. BJ».: Vorbees, CV.. eds. (1988)
    Handbook of behavioral teratology. New
    York: Plenum Press.
Rodier, P.M. (1978) Behavioral teratology. In:
    Wilson. J.G.; Fnser. P.O. eds. Handbook
    of teratology. voL 4. New York: Plenum
    Press, pp. 397-428.
Rodier. P. (1990) Developmental
    neurotoxicology. ToxicoL PathoL 18:89-
    95.
Salsburg, D.S. (1988) Statistics for
    lexicologists. Hew Yoric Marcel Oekkar.
    Inc.
.Sent. W.F. (1987) Complexity of
    neurptoxicological assessment •
    NeurotoxicoL TeratoL 9:411-416.
Sette. W.F.; MacPhail. R.C (1992) Qualitative
    and quantitative issues in assessment of
   . neurotoxic effects. In: TUson. H.;
    Mitchell. O. eds. Target organ toxicity
    series: neurotoxicology, 2nd ed. New
    York: Raven Press, pp. 345-361.
Siegel. S. (1956! Nonparametnc stat'.sciv.j -or
    the behavioral sciences. New York:
    McGraw-Hill.
Silbergeld. E.K.; Percival. R.V. (1987) The
    organometals: impact of accidental
    exposure and experimental data on
    regulatory policies. In: Tilson. H.A.:
    Sparber. S.B.. eds. Neurotoxicants and
    neurobiological function: effects of
    organoheavy metals. New York: J. Wiley.
    pp. 328-352.
Sokal. R.R.; Rohlf. F.J. (1969) Biometry. San
    Francisco: W.H. Freeman and Company.
Spencer, S.; Schaumburg, H.H. (1980)
    Experimental and clinical
    neurotoxicology. Baltimore: Williams
    and Wilkins.        !
Stanton, M.E.: Spear. L.P. (1990) Workshop
    on the qualitative and quantitative
    comparability of human and anim.a.1
    developmental neurotoxicity. Workgroup
    I report Comparability of measures of
    developmental neurotoxicity-jln human*
    and laboratory animals. Neurotoxicol.
    TeratoL 12:261-267.
Sterman, A.B.; Schaumberg, H.H. (1980) The
    neurological examination. In: Spencer,
    P.S.; Schaumberg, H.H.. eds.
    Experimental and clinical
    neurotoxicology. Baltimore: Williams
    and Wilkins, pp. 675-680.
Susser, M. (1986) Rules of inference in
    epidemiology. ReguL ToxicoL
    PharmacoL 6:116-128.
Tilson. RA. (1987) Behavioral indices of
    neurotoxicity: what can be measured?
    NeurotoxicoL Teratol. 9:427-443.
Tilson. H.A. (1990) Neurotoxicology in the
    1990s. NeurotoxicoL Teratol. 12:293-
    300.
Tilson. H.A.: Moser. V.O (1992) Comparison
    of screening approaches.
    Neurotoxicology 13:1-14.
U.S. Environmental Protection Agency.
    (1986) Triethytene glycol monomethyi,
   ' monoethyi. and monobutyl ethers;
    proposed test rule. Federal Register
    51:17883-17894.
U.S. Environmental Protection Agency.
    (1987. May 20) Toxic Substances Control
    Act testing guidelines. 50 FR 39397,
    September 27,1985 as amended. 40 CFR
    798.6050. Federal Register 52:19082.
U.S. Environmental Protection Agency.
    (1988a) Diethylene glycol butyl ether and
    diethylene glycol butyl ether acetate;
    final test rule. Federal Register 53:5932-
    5953.
U.S. Environmental Protection Agency.
    (1988b) Proposed guidelines for
    assessing male reproductive risk. Federal
    Register 53:24850-24869.
U.S. Environmental Protection Agency.
    (1989) FIFRA accelerated reregistration
    phase 3 technical guidance. Appendix D.'
    Office of Prevention. Pesticides and
    Toxic Substances, Washington. DO EPA
    No. 540/09-90-078. Available from:
    NTIS, Springfield. VA. PB-90-161530.

-------
52056
Federal Register  /  Vol. 60,  No.  192  /  Wednesday. October 4.  1995  / Notices
U.S. Environmental Protection Agency.  •
    (1991a) Pesticide assessment guidelines.
    subdivision F. Hazard evaluation: human
    and domestic animals. Addendum 10:
    Neurotoxicity. senes 81,82. and 83.
    Office of Prevention, Pesticides and
    Toxic Substances. Washington, DC EPA
    540/09-91-123. Available from.- NTIS.
    Springfield. VA. PB91-154617.
U.S. Environmental Protection Agency.
    (1991b) Guidelines for developmental
    toxicity risk assessment Federal
    Register 56:63798-63826.
U.S. Environmental Protection Agency.
    (1992) Guidelines for exposure
    assessment Federal Register 57:22888-
    22938.
U.S. Environmental Protection Agency.
    (1994) Final report: principles of
    QBurotoxlcology risk assessment Federal
    RegUttr 59:42350-42404.
                        U.S. En virc-mental Protection Agency.
                            [1995a) The Use of the Benchmark Dose
                            Approach hi Health Risk Assessment.
                            Office of Researcirand Development,
                            Washington, DC EPA/630/R-94/007.
                        U.S. Environmental Protection Agency.
                            (I995b) Policy for Risk Characterization.
                            Office of the Administrator. Washington:.
                            DC
                        U.S. Environmental Protection Agency.
                            (1995c) Guidance for Risk
                            Characterization. Science Policy Council.
                            Washington, DC
                        Valciukas, J.A. (1991) Foundations of
                            environmental and occupational
                            neurotoxicology. New York: Van
                            Nostrand Reinhold.
                        Vorhees, CV. (1987) Reliability, sensitivity
                            and validity of indices of neurotoxicity.
                            NeurotoxicoL TeratoL 9:445-464.
Winer. B.J. (1971) Statistical principles in
    experimental design. New York:
    McGraw-Hill.
Winneki, G. (1995) Endpoints of
    developmental neurotoxicity in
    environmentally exposed children.
    Toxicol. Lett. 77:127-136.
World Health Organization. (1986) Principles
    and methods for the assessment of
    neurotoxicity associated with exposure
    to chemicals. In: Environmental Health
    Criteria Document 60. Geneva: World
    Health Organization.

(FR Doc, 95-246S2 Filed 10-3-95; 8:45 ami
BaiMQCOM tMO-tO-*>

-------