&EPA
United States Environmental
Protection Agency
 Chemical Safety and
Pollution Prevention
 (7101)
EPA 712-C-13-001
 December 2012
       Product Performance
       Test Guidelines
       OCSPP 810.2700:
       Products with Prion-
       Related Claims

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                                     NOTICE
This guideline is  one of a series  of test guidelines established by the United States
Environmental Protection Agency's Office of Chemical Safety and  Pollution Prevention
(OCSPP)  for use  in testing pesticides and chemical substances to develop data for
submission to the Agency under the Toxic Substances Control Act (TSCA) (15  U.S.C. 2601,
et seq.), the  Federal Insecticide, Fungicide and Rodenticide Act (FIFRA) (7 U.S.C.  136, et
seq.), and section 408 of the Federal Food,  Drug and Cosmetic Act (FFDCA) (21 U.S.C.
346a).  Prior to April 22,  2010, OCSPP was known as the Office of Prevention, Pesticides
and Toxic Substances (OPPTS). To distinguish these guidelines from guidelines issued by
other organizations, the numbering convention adopted in 1994 specifically included OPPTS
as part of the guideline's number. Any test guidelines developed after April 22,  2010 will use
the new acronym (OCSPP) in their title.

The OCSPP  harmonized test guidelines serve as a compendium of accepted scientific
methodologies and protocols that are intended to provide data to inform regulatory decisions
under TSCA,  FIFRA,  and/or FFDCA. This document provides guidance for conducting the
test, and is  also used by EPA, the  public,  and the  companies that are subject to data
submission requirements under TSCA, FIFRA, and/or the FFDCA. As a guidance document,
these guidelines are not binding on either  EPA or any outside parties, and the EPA may
depart from the guidelines where circumstances warrant and without prior notice. At places
in this guidance, the Agency uses the word "should."  In this  guidance, the use of "should"
with regard to an action means that the action is recommended rather than mandatory. The
procedures contained in  this guideline are  strongly recommended for generating the data
that are the subject of the guideline, but EPA recognizes that departures may be appropriate
in specific situations.You may propose alternatives to the recommendations  described in
these guidelines, and the Agency will assess them for appropriateness on a case-by-case
basis.

For additional information  about these  test guidelines and to  access  these  guidelines
electronically, please go  to  http://www.epa.gov/ocspp  and select  "Test  Methods &
Guidelines"  on  the  navigation  menu.  You  may  also   access  the  guidelines  in
http://www.regulations.gov grouped by Series under Docket ID  #s: EPA-HQ-OPPT-2009-
0150 through EPA-HQ-OPPT-2009-0159, and EPA-HQ-OPPT-2009-0576.

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OCSPP 810.2700: Products with Priori-Related Claims.

(a) Scope—

   (1) Applicability. This guideline describes test methods that EPA believes will
      generally satisfy certain testing requirements of the Federal Insecticide,
      Fungicide, and Rodenticide Act (FIFRA) (7 U.S.C. 136, etseq.), and the Federal
      Food, Drug, and Cosmetic Act (FFDCA) (21 U.S.C., 301 etseq.).

   (2) Background. Prion ("proteinaceous infectious particle") is a term often used to
      designate an infectious agent that causes progressive degenerative diseases of
      the central nervous system, which are collectively called the transmissible
      spongiform encephalopathies (TSEs or prion diseases), including scrapie,
      chronic wasting disease (CWD), bovine spongiform encephalopathy (BSE), and
      various forms of Creutzfeldt-Jakob disease (CJD), etc. These infectious particles,
      which accumulate in brain tissue during the incubation periods of TSEs, are
      comprised of abnormal folding conformations of a normal, ubiquitous protein
      called the "cellular" prion protein (PrPc).  This normal cellular prion protein is
      synthesized and eventually degraded through normal metabolic processes. In
      certain instances,  however, protein molecules may become misfolded. When
      prion proteins misfold (hereafter called "prions"), the resultant shape change
      serves as a template to induce the misfolding of the normal cellular prion  protein
      to produce more infectious prions and, thereby, propagate  an infection. These
      abnormal prions resist proteosomal degradation and slowly accumulate in the
      brain and infect brain tissue.

      The first described prion disease was scrapie, and so such infectious proteins
      are often designated collectively as PrPSc in all TSEs. Some scientists prefer to
      use other terms such as PrPres, PrPd, PrPTSE, PrPCWD, and PrPCJD to designate
      the specific, abnormal forms of PrP associated with specific prion diseases.

      For purposes of this guidance, the terms "prions" and "TSE agents" are
      synonymous. These abnormal prion  proteins, although  somewhat variable, share
      properties that distinguish them from normal PrPc: they are usually insoluble in
      non-denaturing detergent-salt solutions and relatively resistant to digestion with
      the enzyme proteinase K. These properties are attributed to misfolding of PrPc to
      yield isoforms that are enriched in beta-sheet secondary structure. Many
      scientific experts have concluded that the abnormal prion proteins themselves
      are the self-replicating infectious agents causing TSEs (Prusiner 1982, 2004);
      however, there remain notable reservations, as outlined by Manuelidis (2007a,
      b).

             1.  Manuelidis L. 2007a. A 25 nm virion is the likely cause of
             transmissible spongiform encephalopathies. Journal of
             cellular biochemistry; 100(4):897-915.
             2.  Manuelidis L, Yu ZX, Barquero  N, Mullins B. 2007b.
             Cells infected with scrapie and Creutzfeldt-Jakob disease
             agents produce intracellular25-nm virus-like particles.

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            Proceedings of the National Academy of Sciences of the
            United States of America; 104(6): 1965-70.
            3. Prusiner SB. 1982. Novel proteinaceous infectious
            particles cause scrapie. Science; 216:136-44.
            4. Prusiner SB. 2004. Detecting mad cow disease. Scientific
            American; 291(1):86-93.

(b) Purpose. This guideline provides pesticide applicants and registrants guidance on
test systems and performance standards that apply to pesticide products intended to
reduce the infectivity of prions on inanimate, environmental surfaces (hereafter called
"prion-related products"). EPA encourages pesticide applicants and registrants to follow
this guidance and submit a draft test protocol to EPA for review prior to conducting any
studies. EPA may revise this guidance over time, as needed, to reflect advances in
available test methods and scientific knowledge pertaining to prions. Studies conducted
under this guideline are to be completed under EPA's Good Laboratory Practice
regulations (40 CFR Part 160).

(c) Guidance—

   (1) Labeling Claims. Testing conducted according to currently available test
      methods are adequate for measuring reduction in prion infectivity, but not for
      demonstrating complete  destruction or inactivation of prions. Accordingly, claims
      such as "inactivates," "destroys," "denatures" and "eliminates" are not supported
      by currently available test methods. Further, a prion-related claim  should include
      the type of prion against  which the product has been successfully tested.
      Assuming acceptable data were available, the following is the general format for
      a claim that EPA may consider accepting:

          "Has been demonstrated to reduce infectivity of prions (TSE agents) by (X)
          logs (insert log reduction number supported by data) based on a bioassay of
          the  (insert prion type) in (insert type of organism in which the prions were
          tested)."

      An example of a claim that EPA could find to be acceptable depending  on
      supporting data would be:

          "Has been demonstrated to reduce infectivity of prions (TSE agents) by six
          (6) logs based on a bioassay  of the scrapie prion in transgenic mice."

   (2) Selecting a Test System. The test system should be appropriate to the uses
      that appear on the proposed label.

      a. Carrier-based Method. If the intended uses of a product are for reducing the
      infectivity of prions on inanimate surfaces,  then a carrier-based, animal  bioassay
      should be used to measure the amount of prion infectivity reduction  that is
      achieved by the product  when used according to  label directions. Examples of
      published, carrier-based  test methods include:

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             1.  Lemmer K, Mielke M, Kratzel C, Joncic M, Oezel M, Pauli G, Beekes
             M. Decontamination of surgical instruments from prions. II. In vivo
             findings with a model system for testing the removal of scrapie infectivity
             from steel surfaces. J Gen Virol. 2008 Jan;89(Pt 1):348-58.

             2.  Peretz D, Supattapone S, Giles K, Vergara J, Freyman Y, Lessard P, Safar
             JG, Glidden DV, McCulloch C, Nguyen H-OB, Scott M, DeArmond SJ, and
             Prusiner SB. 2006. Inactivation of prions by sodium dodecyl sulfate. J. Virol.
             80:322-331.

             3.  Weissmann C, Enari M, Klohn PC,  Rossi P, Flechsig E. 2002. Transmission
             of prions. J Infect Dis 186 Suppl 2:5157-65.

             4.  Zobeley E, Flechsig E, Cozzio A, Enari M, and Weissman C. 1999. Infectivity
             of scrapie prions bound to a stainless steel surface. Molecular Medicine 5:240-
             243.

      b. Suspension-based Test Method. If the intended use of a product includes
      only treating liquids (e.g.,  liquid wastes), then a suspension-based, animal
      bioassay should be used to measure the amount of prion infectivity reduction that
      is achieved by the product when used according to label directions. An example
      of a published, suspension-based test method is:

             1.  Peretz D, Supattapone S, Giles K, Vergara J, Freyman Y, Lessard P, Safar
             JG, Glidden DV, McCulloch C, Nguyen H-OB, Scott M, DeArmond SJ, and
             Prusiner SB. 2006. Inactivation of prions by sodium dodecyl sulfate. J. Virol.
             80:322-331.

   (3) Methods of Estimating the Reduction of Prion Infectivity. Prion diseases are
      generally characterized by a long asymptomatic incubation period, followed by
      the rapid  onset of symptoms, followed by death. The length of the incubation
      period is reproducible upon repeated passages of a given prion and is inversely
      proportional to the log of the infectious dose of that prion, although at both very
      high and very low concentrations of infectivity the relationship is no longer linear.
      Two methods of estimating the reduction of prion infectivity have been employed:
      endpoint titration and incubation time interval assay.  The former method may
      be best suited to analyze suspension-based testing and the latter may be best
      suited for carrier-based testing. Further, incubation time interval assays are
      generally not quite as accurate as endpoint titration assays (0.5 log difference1),
      and may be less reliable for quantifying very low levels of infectivity.

      a. End-point Titration. An end-point titration is a classical method of determining
      the titer of a sample (i.e., the concentration of the pathogen). To begin with, a
1 Prusiner SB, Cochran SP, Downey DE, Groth DF. Determination of scrapie agent titer from incubation
period measurements in hamsters. Adv. Exp. Med. Biol. 1981;134: 385-99.

Prusiner SB, Cochran SP, Groth DF, Downey DE, Bowman KA, Martinez HM. Measurement of the
scrapie agent using an incubation time interval assay. Ann. Neurol. 1982 Apr;11(4):353-8.

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sample is serially diluted by a factor of 10 until less than 1  ID50 (the infectious
dose which kills 50% of the pathogen) remains in the final  dilution. The resulting
set of serial dilutions is used to inoculate a corresponding set of experimental
animals, typically at least four animals per 10-fold dilution.  The experimental
animals are observed for the appearance of symptoms, and the symptoms are
scored. The animals are observed for a predetermined period, usually 450 days
for hamsters or 500 days for mice. At the end of the predetermined period, any
surviving animals would be humanely euthanized before they would die of the
prion disease and given a thorough neuropathological examination that looks for
signs of prion disease as described in section (4) below. The titer may be
determined by several statistical methods (see references below). The titers of
subsequent samples are determined in the same fashion.

The following are examples of end-point titration methods:

             1. Andersen J, Barrett T, Scott GR. 1996. Appendix 3. Fifty percent
             effective dose (ED50): Spearman-Karber method. In Manual of the
             Diagnosis of Rinderpest. (FAO Animal Health Manual - 1) Food and
             Agriculture Organization of the United Nations. Rome. Available on-line:
             http://www.fao.org/docrep/w0049e/w0049e07.htmtfappendix%203.%20fift
             v%20percent%20effective%20dose%20(ed50):%20spearman%20karber
             %20method

             2. Reed LJ and Muench H. A simple method for estimating fifty percent
             endpoints. Amer J Hyg 1938;27:493-7.

             3. Bliss Cl. The method of probits. Science. 1934 Jan 12;79(2037):38-39.

b. Incubation Time Interval Assay. An  incubation time interval assay exploits
the relationship between the length of the incubation period and the titer of the
pathogen in an inoculum. An endpoint titration of a starting brain homogenate is
used to establish an empirical relationship between prion titer and length of
incubation period. Once the relationship  is established, the titer of any
subsequent sample is determined by observing the incubation period of an
inoculated animal group (usually at least four) and using this value to predict a
corresponding titer based on the empirically determined  relationship. The initial
endpoint titration should not be greatly, if at all, separated  in time from the
experimental  assay. If the initial endpoint titration is to be replaced with  historical
animal model data, then sufficient control animals should be included to ensure
that the historical animal model data are relevant to the experimental assay.

      The following are examples of incubation time interval assay methods:

             1. Prusiner SB, Cochran SP, Groth DF, Downey DE, Bowman  KA,
             Martinez HM. 1982. Measurement of the scrapie agent using an
             incubation time interval assay. Ann. Neurol. April; 11(4):353-8.

             2. Prusiner SB, Cochran SP, Downey DE, Groth DF. 1981.
             Determination of scrapie agent titer from incubation period measurements
             in hamsters. Adv Exp Med Biol. 134:385-99.

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      The endpoint titration and incubation time interval assays yield similar results;
      however, the endpoint titration requires many more animals. As a result, the
      incubation time interval assay is the more widely used assay method for prions
      since it is faster, uses fewer animals, and provides results that are negligibly
      different (± 0.5 log)2 compared to the endpoint titration. However, an endpoint
      titration assay may be more useful than an incubation time assay if the difference
      between the titer of the prions in the starting inoculum and the treated carrier is
      very high or very low, or if one wants to directly compare two samples with
      similar titers. A comparison of the number of animals required for these assays is
      listed in Appendix 1. The 263K strain of hamster-adapted scrapie is being
      provided as an example. The endpoint titration requires between two and four
      times the animals as the incubation time  interval  assay.

      c. Other Relevant Tests. EPA welcomes data from screening tests (such as
      Western blot, ELISA, Protein Misfolding Cyclic Amplification (PMCA), or cell
      culture assays),  but such tests are not a substitute for the suspension-based or
      carrier-based tests.

   (4) Other important aspects  of the test system include the following:

      Titer of prions:  Depending on the test method and type of prion used, the titer
      of the prions in the initial inoculum may range from 104to 1011 ID50 units/g of
      brain homogenate, based on currently available studies.  After dilution and drying
      of the inoculum on the carrier or in a suspension, the titer of the prions  may be
      further reduced by 1-2 logs. The study should have a reliable method for
      determining the concentration of prions in the initial inoculum and the
      concentration of prions dried on the carrier or mixed in a suspension. The
      dynamic range of the test method's ability to measure reduction in infectivity
      should be well established. In order for the test to be able to measure at least a
      six  (6) log reduction in infectivity [see section (5)  Evaluation of Success below],
      the titer of the prions on the carrier or in a suspension (i.e., the titer to which test
      animals will be exposed) should be at least 107 ID50 units/g brain homogenate (or
      about 109 ID50 units/g brain homogenate in the initial inoculum). Finally, the
      protocol should address and balance such issues as the preparation of the  initial
      inoculum, the order in which animals are  inoculated, and how the animals are
      housed (see Animal Housing below).

      Prion type: Several types of prions are available for use in infectivity tests, such
      as scrapie prions (hamster adapted 263K), BSE prions (mouse adapted 301V,
      31OC and 6BP1), and sCJD prions (human). An animal-related prion (e.g.,
      scrapie, CWD) should be selected for testing if the proposed  use sites are
      animal-related (e.g., farm premises, farm equipment, veterinary clinics). A
      human-related prion (e.g., sCJD) should be selected if the proposed use sites
      are related to humans (e.g., surgical instruments, hospital rooms, laboratories).
      [Note:  Prospective registrants should consult with the U.S. Food and Drug
      Administration (FDA) for uses that are also under its jurisdiction (e.g., medical

2 See references in footnote 1.

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devices or adjuncts to medical devices). The FDA considers claims of activity
against prions (TSE agents) to be unique and unclassified, and recommends that
product manufacturers seeking a product claim of reducing the infectivity of
prions (TSE agents) for any healthcare use meet with FDA to learn the FDA's
recommendations for seeking product approval.] Human-derived TSE materials
of a known titer currently are available at only a few research laboratories.

Age of test animals at beginning of study: Animals should be old enough to
tolerate intracerebral inoculation without excessive mortality, i.e., in the following
age ranges: mice, 6-10 weeks old; hamsters, 5-8 weeks old; and guinea pigs, 5-7
weeks  old. The study should continue up to the end of the animals' normal life
span (the point at which normal mortality begins to increase significantly).
Historical mortality data on the selected strain of test animals should  be provided
to substantiate the selection of these critical lifespan points.

Number of animals:  The numbers of animals in the treatment and control
groups should be sized based on statistical validity, and the calculations
supporting the proposed  animal group sizes should be included. The number of
animals typically  used is  between  4 and 24.

Types/Species of animals: The type/species of animal is determined by the test
method selected. The test animals are either genetically homogeneous mice or
hamsters,  or transgenic (genetically altered to express the prion protein—PrP—
of the host animal) mice or hamsters. If the animals are transgenic, the test
protocol should identify the source of the transgenic gene material  and available
information that characterizes it. Native species of prions may also be tested in
relevant animal species.

Animal housing and environmental conditions: The number of  animals per
cage should be kept to a minimum and the cages should be compatible with the
animals. Other animal housing issues should be addressed to avoid influencing
the test results; for example, such as which groups may be housed next to each
other, and rotating cages to balance exposure to heat, light, noise,  etc.
Transgenic or wild-type mice can be housed 5-8 per cage, depending on the size
of the cage, and hamsters are generally housed two per cage. The temperature
in the experimental animal room should be 22°C (± 3°C). The relative humidity
should  be  at least 30% and preferably not exceed 70% other than during room
cleaning. Lighting should be artificial, the sequence being 12 hours light and 12
hours dark.

Length of study: The  study should  be extended as long as possible, taking into
account the historical mortality data for the particular animal type/species used.
Transgenic or wild-type mice should be kept for 500 days. Hamsters  should be
kept for 450 days.

Examination of animals at end of study or when animals die prematurely:
When animals reach the  defined age limit or die prematurely, tests should be
performed on all members of both the treated and control groups, in order to
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ascertain whether they are infected with prions. Such tests should include at
least one of the following: Western blot, immunological histochemistry or "blind
passage." The method for dealing with premature deaths and how to place them
into the statistical calculations should also be addressed in the statistical
evaluation plan for the study.

Evaluation of Success: The target criterion for success is no less than six  (6)
logs of reduction of infectivity in the treated versus untreated (control) groups.

Submission of Draft Protocol: Due to the wide variety of available animal
bioassays for measuring reduction of prion infectivity by a prion-related product
on environmental surfaces, the Agency strongly recommends that the registrant
submit a draft test protocol to EPA for review prior to conducting such a study.
The Agency also recommends that the registrant request a pre-registration
conference to discuss registration data and labeling requirements for a prion-
related product.

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  Appendix 1. Animals used in an endpoint titration versus an incubation time interval
                      assay under different sets of assumptions

Assuming:

   •   Initial brain titer of 1010 ID50/g
   •   10 treatments are evaluated.
   •   6 animals are used per log dilution.
   •   Each treatment reduces infectivity by 104.

  Endpoint titration:

   Initial  titration (10 log dilutions)                                    10x6= 60
   10 x Titration of each treatment  (7 log dilutions)                 10x7x6 = 420
   Total                                                                 480

  Incubation time interval assay:

   Titration/calibration curve (10 log dilutions)                         10x6= 60
   10x1 group per treatment                                      10x6= 60
   Total                                                                 120

Same assumptions except:

   •   Each treatment reduces infectivity by 106.

  Endpoint titration:

   Initial  titration (10 log dilutions)                                    10x6= 60
   10 x Titration of each treatment  (5 log dilutions)                 10x5x6 = 300
   Total                                                                 360

  Incubation time interval assay:

   Titration/calibration curve (10 log dilutions)                         10x6= 60
   10x1 group per treatment                                      10x6= 60
   Total                                                                 120

Same assumptions except:

   •   Each treatment reduces infectivity by 108.

  Endpoint titration:

   Initial  titration (10 log dilutions)                                    10x6= 60
   10 x Titration of each treatment  (3 log dilutions)                 10x3x6= 180
   Total                                                                 240

  Incubation time interval assay:

   Titration/calibration curve (10 log dilutions)                         10x6= 60
   10x1 group per treatment                                      10x6= 60
   Total                                                                 120

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